Figure 2 | Laboratory Investigation

Figure 2

From: Long-Chain L-3-Hydroxyacyl-Coenzyme A Dehydrogenase Deficiency: A Molecular and Biochemical Review

Figure 2

Mitochondrial β-oxidation of fatty acids. The enzymes long-chain 2,3-enoyl-coenzyme A (CoA) hydratase (LHYD), long-chain l-3-hydroxyacyl-CoA dehydrogenase (LCHAD), and long-chain 3-ketoacyl-CoA thiolase (LKAT) are components of membrane-bound mitochondrial trifunctional protein (MTP). The medium- and short-chain homologs of these enzymes are nonmembrane–bound discrete proteins. VLCAD = very long-chain acyl-CoA dehydrogenase.

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