TABLE 1 Summary of Clinical Data and Follow-Up of Present and Previously Reported Cases
Case | Age, Sex | Presenting Symptoms | Site, Imaging Features | Bone Involvement | Surgery | Staging | Adjuvant Therapy | Follow-Up |
|---|---|---|---|---|---|---|---|---|
1 | 17, M | Headache | R frontal, 5-cm dura-based mass, enhancing | No | GTRa | Neg | Local RT | NED for 8 y |
Dizziness, ataxia, L-sided tinnitus | L CPA mass recurrence, nonhomogeneuosly enhancing | No | STRa | Neg | Systemic chemotherapy, craniospinal RT | No progression at 12 mo | ||
2 | 12, M | Severe headache, L neck, arm, chest parasthesias | R frontal, 4.5-cm dura-based mass, enhancing | No | GTR | Neg | Chemotherapy, craniospinal RT | NED at 27 mo |
3b | 30, F | Headache and vertigo | R frontal, 2 dura-based masses (4 and 7 cm), enhancing | No | GTR | Not done | None (diagnosis, meningioma) | NED for 7 y |
Unknown | Local recurrence | Unknown | GTR | Not done | None (diagnosis, HPC) | NED for 2 y | ||
Chest and sacro-iliac pain | L 7th rib, T8, L2 and L3 metastases | Yes | L 7th rib biopsy | Chemotherapy, RT | Died 1 y later, 10 y after 1st diagnosis | |||
4c | 5, M | Vomiting, mild L VI nerve palsy | Large tentorial mass | No | GTR | Neg CSF | Intrathecal chemotherapy, RT | NED at 7 y |
5d | 6, M | “Paroxysmal event” | L frontal | No | GTR | Neg | Recommended chemotherapy, RT | Not available |
