Table 4 Relapses/progressions in 22 stage 2 patients without MYCNA

From: Treatment of localised resectable neuroblastoma. Results of the LNESG1 study by the SIOP Europe Neuroblastoma Group

Case no.

Age (months)

Primary site

INSS stage

Histopathology

LDH

Ploidy

Site/time to relapse/progression

Therapy

Outcome

 1

0

P

2A

U

N

An

Local, 6 months

None

CR, 134 months

 2

0

P

2B

F

Local, 2 months

CT

LFU, 20 months

 3

1

A

2B

F

N

An

Local, 5 months

CT

DOD, 10 months

 4

2

A

2A

F

N

An

Local, 1 month

CT

DOD, 10 months

 5

2

T

2A

F

N

Te

Local, 4 months

CT

CR, 105 months

 6

2

A

2B

F

N

D

Local, BM, 7 months

CT

CR, 88 months

 7

3

A

2B

U

N

An

Local, BM, 8 months

CT, S

CR, 112 months

 8

3

P

2A

F

Local, Skin 6 months

CT, S

CR, 125 months

 9

6

A

2B

F

N

An

Local, 14 months

CT

CR, 88 months

10

9

P

2B

F

N

An

Local, 13 months

CT

CR, 38 months

11

10

A

2B

F

N

An

B, BM, 6 months

CT, RT

LFU, 27 months

12

10

A

2A

F

N

Te

Local, 9 months

RT

Unknown

13

13

A

2A

Local, 15 months

CT

CR, 55 months

14

14

Neck

2B

F

An

Local, 1 month

CT, S

CR, 89 months

15

27

A

2A

U

E

Te

Local, B, Lung, 2 months

CT, S

DOD, 27months

16

42

T

2A

U

N

Te

Local, BM, B, 4 months

CT, S

DOD, 46 months

17

43

A

2B

U

E

Te

Local, 1 month

CT, S

DOD, 57 months

18

47

T

2B

F

N

Local, BM, 3 months

CT, S

DOD, 19 months

19

55

A

2B

U

N

Local, 36 months

CT, S

DOD, 77 months

20

65

A

2B

U

E

D

Local, B, 5 months

S, CT

DOD, 32 months

21

68

T

2A

U

N

Local, 26 months

None

CR

22

100

P

2B

U

N

D

Local, B, Liver, 92 months

None

LFU, 93 months

  1. A=abdomen; An=aneuploid; B=bone; BM=bone marrow; CR=complete remission; CT=chemotherapy; D=diploid; DOD=dead of disease; E=elevated; F=favourable; LFU=lost to follow-up; N=normal; P=pelvis; RT=radiotherapy; S=surgery; T=thorax; Te=Tetraploid; U=unfavourable.