Table 4 Relapses/progressions in 22 stage 2 patients without MYCNA
Case no. | Age (months) | Primary site | INSS stage | Histopathology | LDH | Ploidy | Site/time to relapse/progression | Therapy | Outcome |
---|---|---|---|---|---|---|---|---|---|
1 | 0 | P | 2A | U | N | An | Local, 6 months | None | CR, 134 months |
2 | 0 | P | 2B | F | — | — | Local, 2 months | CT | LFU, 20 months |
3 | 1 | A | 2B | F | N | An | Local, 5 months | CT | DOD, 10 months |
4 | 2 | A | 2A | F | N | An | Local, 1 month | CT | DOD, 10 months |
5 | 2 | T | 2A | F | N | Te | Local, 4 months | CT | CR, 105 months |
6 | 2 | A | 2B | F | N | D | Local, BM, 7 months | CT | CR, 88 months |
7 | 3 | A | 2B | U | N | An | Local, BM, 8 months | CT, S | CR, 112 months |
8 | 3 | P | 2A | F | — | — | Local, Skin 6 months | CT, S | CR, 125 months |
9 | 6 | A | 2B | F | N | An | Local, 14 months | CT | CR, 88 months |
10 | 9 | P | 2B | F | N | An | Local, 13 months | CT | CR, 38 months |
11 | 10 | A | 2B | F | N | An | B, BM, 6 months | CT, RT | LFU, 27 months |
12 | 10 | A | 2A | F | N | Te | Local, 9 months | RT | Unknown |
13 | 13 | A | 2A | — | — | — | Local, 15 months | CT | CR, 55 months |
14 | 14 | Neck | 2B | F | — | An | Local, 1 month | CT, S | CR, 89 months |
15 | 27 | A | 2A | U | E | Te | Local, B, Lung, 2 months | CT, S | DOD, 27months |
16 | 42 | T | 2A | U | N | Te | Local, BM, B, 4 months | CT, S | DOD, 46 months |
17 | 43 | A | 2B | U | E | Te | Local, 1 month | CT, S | DOD, 57 months |
18 | 47 | T | 2B | F | N | — | Local, BM, 3 months | CT, S | DOD, 19 months |
19 | 55 | A | 2B | U | N | — | Local, 36 months | CT, S | DOD, 77 months |
20 | 65 | A | 2B | U | E | D | Local, B, 5 months | S, CT | DOD, 32 months |
21 | 68 | T | 2A | U | N | — | Local, 26 months | None | CR |
22 | 100 | P | 2B | U | N | D | Local, B, Liver, 92 months | None | LFU, 93 months |