Table a1 Clinical Characteristics of 125 from 142 Infants with Kernicterus Discharged as Healthy (Pilot Kernicterus Registry)
From: Kernicterus: Epidemiological Strategies for Its Prevention through Systems-Based Approaches
Source/code | Birth year | BW (g) | GA (weeks) | Sex/race | Discharge day | Readmit age (day) | Readmit TSB | Peak TSB | Acute BIND | Ex Tx | Photo Rx | Likely cause | Follow-up | Icteric sequelae | Comments |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
C-001 | 1994 | 3260 | 36 | m/W | 0.5 | 4.0 | 35.0 | 35.0 | Advanced | Yes | Yes | Idiopathic | Yes | Moderate | ABO Coombs neg |
C-002 | 1993 | 3725 | 39 | m/A | 0.5 | 4.0 | 40.2 | 40.2 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | ABO Coombs pos |
L-003 | 1988 | 3785 | 39 | unk/H | 0.5 | 4.0 | 45.0 | 45.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | ExTx delayed 12 hours. (Jehovah Witness) |
M-004 | 1996 | 3000 | 36 | f/B | 0.5 | 4.5 | 40.9 | 40.9 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Hct 45%, wt loss |
M-005 | 1997 | 3884 | 38 | m/W | 0.5 | 5.0 | 46.0 | 46.0 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | ABO Coombs neg, jaundice <24 hours age, Na 149 mEq/L |
M-006 | 1993 | 3856 | 41 | f/W | 1.0 | 2.5 | 22.4 | 22.4 | Advanced | No | Yes | Idiopathic | Yes | Severe | Dehydration, Na 153 mEq/l |
L-007 | 1995 | 3544 | 39 | f/A | 1.0 | 3.0 | 27.8 | 27.8 | Subtle | Yes | Yes | Infection | Yes | None | Urosepsis (E. coli), MRI (at day 5): inc. globus pallidus signal |
M-008 | 1995 | 2920 | 37 | m/B | 1.0 | 3.0 | 33.0 | 36.7 | Advanced | No | Yes | G6PD | Yes | Severe | Hct 40%, Presumed sepsis |
C/M-009 | 1990 | 2015 | 36 | f/W | 1.0 | 3.5 | 41.8 | 41.8 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Plethora, ABO Coombs neg |
M-010 | 1998 | 3629 | 39 | f/W | 1.0 | 3.5 | 52.0 | 52.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Family history, jaundice <24 hours age |
L/C-011 | 1995 | 2614 | 39 | f/B | 1.0 | 4.0 | 33.0 | 33.0 | Moderate | No | Yes | Idiopathic | Yes | Moderate | Hct 43% |
P-012 | 1999 | 4026 | 39 | m/W | 1.0 | 4.0 | 39.0 | 45.0 | Advanced | Yes | Yes | Birth trauma | Yes | Severe | Precipitous labor, family history of jaundice |
P-013 | 2002 | 3714 | 40 | m/W | 1.0 | 4.0 | 44.8 | 44.8 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | Congenital spherocytosis, Hct 27%, peak TSB 49 mg/dl |
P-014 | 2000 | 4200 | 35 | f/W | 1.0 | 5.0 | 27.0 | 31.5 | Subtle | No | Yes | Birth trauma | Yes | Severe | Plethora at birth |
L/C-015 | 1994 | 3489 | 39 | m/W | 1.0 | 5.0 | 30.6 | 30.6 | Advanced | Yes | Yes | Idiopathic | Yes | None | Hct 38%, Albumin before ExTx |
L-016 | 1996 | 2637 | 39 | m/H | 1.0 | 5.0 | 34.8 | 34.8 | Moderate | Yes | Yes | Idiopathic | Yes | None | Hct 48% |
M-017 | 1996 | 3450 | 39 | f/H | 1.0 | 5.0 | 37.0 | 46.0 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | ABO Coombs pos, jaundice <24 hours age |
L-018 | 1993 | 3147 | 39 | m/B | 1.0 | 5.0 | 42.5 | 42.5 | Advanced | Yes | Yes | G6PD | Yes | Severe | Mild anemia, no evident hemolysis |
M-019 | 1992 | 3685 | 39 | m/B | 1.0 | 5.5 | 46.8 | 46.8 | Advanced | No | Yes | G6PD | Died | Died | Moribund on readmission |
C-020 | 1995 | 3130 | 39 | m/H | 1.0 | 6.0 | 28.5 | 28.5 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | ABO, Coombs unk, Hct 42% |
M-021 | 1997 | 3680 | 37 | m/W | 1.0 | 6.0 | 29.3 | 32.5 | Advanced | Yes | Yes | Birth trauma | Yes | Severe | 13% wt loss at day 6, Hct 44% |
M-022 | 1994 | 3048 | 35 | f/W | 1.0 | 6.0 | 31.0 | 31.0 | Advanced | No | Yes | Birth trauma | Yes | Severe | 11% wt loss at day 6 |
P-023 | 2002 | 2745 | 38 | f/W | 1.0 | 6.0 | 46.2 | 46.2 | Advanced | Yes | Yes | Hemolysis | No | Severe | ABO Coombs pos, jaundice <24 hours age |
P-024 | 1993 | 3487 | 37 | m/H | 1.0 | 8.5 | 41.3 | 53.9 | Advanced | Yes | Yes | Birth trauma | Yes | Severe | Hct 43% |
P-025 | 1994 | 3090 | 37 | m/W | 1.0 | 12.0 | 41.0 | 41.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | ABO Coombs neg 17% wt loss (day 12) |
P-026 | 1997 | 3433 | 39 | m/W | 1.0 | None | None | None | Moderate | No | No | Idiopathic | Yes | Moderate | ABO, Coombs: unk, prolonged jaundice (>8 weeks) |
M-027 | 1993 | 3355 | 37 | f/W | 1.0 | None | Not done | None | Advanced | No | No | Hemolysis | Yes | Severe | ABO Coombs: unk,16% wt. loss d15, arching (at age 1 week), Peak TSB unk |
C-028 | 1999 | 3720 | 40.5 | m/B | 1.5 | 3.0 | 21.4 | 21.4 | Moderate | No | Yes | Idiopathic | Lost | UNK | Lost to follow-up |
C-029 | 1991 | 2865 | 39 | m/H | 1.5 | 3.0 | 38.4 | 38.4 | Advanced | Yes | Yes | G6PD | No | Severe | Hct 40%, abnormal RBC smear |
M-030 | 1991 | 3374 | 39 | f/W | 1.5 | 3.0 | 38.4 | 44.5 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Hct 52%, father with Gilbert's syndrome |
C-031 | 1998 | 3600 | 37 | f/W | 1.5 | 3.5 | 38.5 | 38.5 | Subtle | Yes | Yes | Idiopathic | <1 yr | Moderate | ABO Coombs neg, Hct 64% |
C-032 | 2001 | 3994 | 38 | m/W | 1.5 | 4.0 | 22.0 | 27.0 | Moderate | Yes | Yes | Idiopathic | Yes | None | 14% wt loss at day 4, Na 152 mEq/l |
M-033 | 1999 | 3510 | 39 | m/B | 1.5 | 4.0 | 33.6 | 37.2 | Moderate | No | Yes | Hemolysis | Yes | Severe | ABO Coombs neg, Hct 41% |
P-034 | 2001 | 3468 | 38.5 | m/W | 1.5 | 4.0 | 38.0 | 41.0 | Advanced | Yes | Yes | Birth trauma | Yes | Severe | Jaundice noted at age 24 hours |
L-035 | 2000 | 3203 | 38 | f/H | 1.5 | 3.0 | 46.9 | 46.9 | Advanced | Yes | Yes | Idiopathic | Yes | None | Sibling treated for jaundice |
P-036 | 2001 | 3572 | 39.6 | m/W | 1.5 | 4.5 | 28.3 | 28.3 | Subtle | No | Yes | Birth trauma | Yes | Severe | Family (sibling) history of jaundice |
M/L-037 | 1991 | 2665 | 36 | f/B | 1.5 | 4.5 | 37.0 | 39.5 | Advanced | Yes | Yes | G6PD | Yes | Severe | Hemolysis trigger unk, Hct 28% |
M-038 | 1996 | 2892 | 36 | f/W | 1.5 | 5.0 | 27.0 | 28.7 | Moderate | No | Yes | Birth trauma | Yes | Severe | Partially treated perinatal sepsis, Hct 50%, Na 150 mEq/l |
M-039 | 1997 | 3985 | 39 | f/A | 1.5 | 5.0 | 30.4 | 37.8 | Advanced | YES | Yes | Birth trauma | Yes | Moderate | ABO Coombs neg,15% wt loss at day 5, Na 152 mEq/l |
C-040 | 1996 | 2500 | 38 | m/B | 1.5 | 5.0 | 41.3 | 41.3 | Advanced | Yes | Yes | G6PD | Died | Severe | Urosepsis, Hct 22%, died at 6 months |
M-041 | 1993 | 2925 | 38 | m/B | 1.5 | 5.0 | 45.9 | 45.9 | Advanced | Yes | Yes | G6PD | Died | Died | Incomplete evaluation of hyperbilirubinemia |
L-042 | 1994 | 2840 | 37 | m/A | 1.5 | 5.0 | 49.2 | 49.2 | Advanced | Yes | Yes | G6PD | Died | Died | 13.6% wt loss at day 5, neutropenia, no hemolysis |
M-043 | 2000 | 3180 | 39 | m/W | 1.5 | 5.0 | 59.9 | 59.9 | Moderate | Yes | Yes | Hemolysis | Yes | Severe | ABO, Coombs pos, jaundice at age 9 hours, wt loss >20% |
M-044 | 1992 | 2380 | 36 | f/A | 1.5 | 5.5 | 32.0 | 32.0 | Advanced | Yes | Yes | Birth trauma | Yes | Severe | 13% wt loss at day 5.5, Plethora, Hct 64% |
M-045 | 1995 | 2863 | 37 | m/W | 1.5 | 5.5 | 34.6 | 34.6 | Advanced | No | Yes | Hemolysis | Yes | Severe | ABO Coombs: unk, otitis media |
C-046 | 1997 | 3650 | 38 | m/A | 1.5 | 6.0 | 25.6 | 25.6 | Advanced | Yes | Yes | G6PD | Yes | None | Albumin before exchange, Hct 50%, Na 154 mEq/l |
M-047 | 2001 | 3310 | 36 | m/H | 1.5 | 6.0 | 33.5 | 33.5 | Subtle | Yes | Yes | Idiopathic | Yes | Severe | Bruising, Hct 42% |
L-048 | 1995 | 3400 | 41 | m/B | 1.5 | 6.0 | 41.0 | 41.0 | Advanced | Yes | Yes | G6PD | Yes | Severe | Concurrent sepsis (E. coli) |
C-049 | 1996 | 4280 | 39 | m/A | 1.5 | 6.0 | 45.7 | 45.7 | Advanced | Yes | Yes | G6PD | Yes | Moderate | Hemolysis trigger: mothball exposure |
L-050 | 1988 | unk | 39 | unk/B | 1.5 | 7.0 | 24.0 | 28.0 | Advanced | Yes | Yes | G6PD | Yes | Severe | Direct bilirubin 9 mg/dl at day 7 |
P-051 | 2002 | 3057 | 38.5 | m/W | 1.5 | 7 | 31.0 | 41.0 | Subtle | No | Yes | Hemolysis | Yes | Moderate | Wt loss: 15%, ABO, Coombs pos |
P-052 | 2000 | 3317 | 36 | m/W | 1.5 | 7.0 | 35.0 | 35.0 | Advanced | Yes | Yes | Hemolysis | Yes | None | Plethora, 17% wt loss at day 7.0 |
C-053 | 1994 | 4455 | 41 | m/W | 1.5 | 7.0 | 42.0 | 42.0 | Advanced | Yes | Yes | Idiopathic | Lost | Severe | Follow-up incomplete |
M-054 | 1990 | 2608 | 36 | m/B | 1.5 | 8.0 | 33.7 | 36.4 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Hct 43% |
P-055 | 1989 | 4224 | 38 | m/W | 1.5 | 8.5 | 37.0 | 39.0 | Moderate | Yes | Yes | Idiopathic | Yes | Severe | Seen by MD at day 7.5, no TSB done |
M-056 | 1995 | 2700 | 36 | m/B | 1.5 | 10.0 | 32.5 | 32.5 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Hct 41% |
C-057 | 1996 | 3150 | 36 | m/W | 1.5 | 11.0 | 40.0 | 40.0 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | Hct 22%, abnormal RBC morphology, hemolysis cause unk. |
P-058 | 1997 | 3033 | 36.5 | m/W | 1.5 | 13.0 | 25.0 | 27.7 | Advanced | No | Yes | Hemolysis | Yes | Severe | Hct 18%, abnormal RBC morphology |
M-059 | 2002 | 3199 | 37 | m/W | 1.5 | 19.0 | 44.7 | 44.7 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Hct 43%, direct bilirubin 1.7 mg/dl |
M-060 | 1994 | 3062 | 37 | m/W | 1.5 | None | 31.6 | 31.6 | Moderate | No | Yes | Hemolysis | Yes | Severe | ABO Coombs pos, home phototherapy day 4 for TSB 31.6 mg/dl |
P-061 | 2000 | 2951 | 38 | f/W | 1.5 | None | Not done | None | Subtle | No | No | Birth trauma | Yes | Severe | First office visit at d12 (TSB=13 mg/dl), peak TSB Unk. |
M-062 | 2001 | 2715 | 37.5 | f/B | 2.0 | 3.5 | 35.0 | 38.4 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | ABO Coombs pos, Hct 31%, retic 18%, Bacteremia g+cocci bacillus species |
M-063 | 2000 | 2438 | 36 | f/W | 2.0 | 3.5 | 35.4 | 35.4 | Advanced | No | Yes | Idiopathic | Died | Died | Plethora, bruising |
M-064 | 1999 | 3626 | 38 | m/B | 2.0 | 3.5 | 39.0 | 44.0 | Moderate | Yes | Yes | G6PD | No | Severe | 9% wt loss at day 3.5, Hct 50% |
M-065 | 2001 | 3260 | 36 | m/B | 2.0 | 4.0 | 33.0 | 34.0 | Subtle | Yes | Yes | Idiopathic | Yes | Severe | ABO Coombs negative, IDM |
M-066 | 1984 | 2850 | 36.5 | m/W | 2.0 | 4.0 | 33.9 | 39.8 | Advanced | Yes | Yes | Birth trauma | Yes | Moderate | Hct 53%, family (sibling) history of jaundice |
M-067 | 1992 | 2825 | 37.5 | m/B | 2.0 | 4.0 | 34.5 | 34.5 | Advanced | No | Yes | Idiopathic | Yes | Severe | Hct 45% |
C-068 | 1995 | 3459 | 39 | m/B | 2.0 | 4.0 | 39.2 | 39.2 | Advanced | Yes | Yes | G6PD | Yes | Severe | Neutropenia, presumed sepsis, Hct 38% |
M-069 | 1993 | 2625 | 40 | M/B | 2.0 | 4.0 | 44.2 | 46.0 | Advanced | Yes | Yes | G6PD | Yes | Severe | Hct 45%, hemolytic trigger: mothball exposure |
L-070 | 1992 | 3400 | 39 | m/H | 2.0 | 4.0 | 50.1 | 50.1 | Advanced | Yes | Yes | G6PD | Yes | Severe | Sepsis (E. coli) |
C/L-071 | 2002 | 2609 | 40 | m/B | 2.0 | 4.5 | 31.7 | 31.7 | Advanced | No | Yes | G6PD | Died | Died | 9% wt loss at day 4.0, Hct 34% |
P-072 | 2002 | 3402 | 38 | m/W | 2.0 | 4.5 | 38.0 | 38.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Jaundice noted before 24 hours age |
L-073 | 1989 | 3150 | 39 | m/W | 2.0 | 5.0 | 28.7 | 29.5 | Subtle | Yes | Yes | Hemolysis | Yes | None | ABO Coombs pos, failed BAER at d/c (passed at 6 months) |
P-074 | 2001 | 2384 | 35 | M/W | 2.0 | 5.0 | 31.0 | 31.0 | Moderate | Yes | Yes | Idiopathic | Yes | Severe | Mom has congenital spherocytosis |
M-075 | 1990 | 2790 | 36.5 | m/W | 2.0 | 5.0 | 36.8 | 39.8 | Advanced | Yes | Yes | G6PD | Yes | Severe | E. coli sepsis, birth trauma, ABO Coombs neg |
M-076 | 1995 | 4687 | 39 | f/H | 2.0 | 5.0 | 37.0 | 46.5 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | ABO Coombs neg, abnormal RBC morphology, Hct 39 |
M-077 | 1991 | 2835 | 36 | f/W | 2.0 | 5.0 | 41.1 | 44.4 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | 20% wt loss at day 5 |
M-078 | 1993 | 3260 | 39 | f/H | 2.0 | 6.0 | 30.2 | 38.0 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | Plethora, hemolysis cause: unk |
M-079 | 1996 | 3350 | 36 | m/W | 2.0 | 6.0 | 34.7 | 34.7 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Hct 56% |
P-080 | 2000 | 3178 | 37.5 | m/W | 2.0 | 6.0 | 35.0 | 42.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | 14% wt loss at day 6 |
C-081 | 1987 | 3175 | 37 | m/W | 2.0 | 6.0 | 41.8 | 41.8 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | 18% wt loss at day 6, Hct 57% |
P-082 | 2002 | 3320 | 37 | f/W | 2.0 | 6.5 | 25.3 | 25.3 | Advanced | No | Yes | Birth trauma | Yes | Moderate | ABO Coombs pos, Hct 51%, jaundice <24 hours |
M-083 | 2000 | 3856 | 37.5 | m/W | 2.0 | 6.5 | 28.6 | 36.2 | Advanced | Yes | Yes | Birth trauma | Yes | Severe | Hct 45% |
M-084 | 1991 | 3310 | 38 | m/B | 2.0 | 7.0 | 21.5 | 36.0 | Advanced | Yes | Yes | G6PD | No | Severe | TSB 36 at day 10.8, nosocomial sepsis day 11 |
C-085 | 1998 | unk | 39 | f/B | 2.0 | 7.0 | 48.0 | 48.0 | Advanced | Yes | Yes | Infection | Yes | Severe | Vomiting for 4 days, intraosseous fluids. Hct 28% |
P-086 | 2002 | 2724 | 37 | m/B | 2.0 | 7.0 | 33.0 | 33.0 | Moderate | Yes | Yes | G6PD | Yes | Moderate | Family (maternal) history of jaundice |
P-087 | 1994 | 3572 | 38 | m/W | 2.0 | 7.0 | 39.0 | 39.0 | Advanced | Yes | Yes | Idiopathic | Yes | Mild | Apneic spells on admission |
P-088 | 1998 | 3263 | 39 | f/W | 2.0 | 7.0 | 42.0 | 42.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Atraumatic forceps delivery |
C-089 | 2002 | 2700 | 35.5 | m/B | 2.0 | 7.0 | 46.2 | 46.2 | Advanced | Yes | Yes | G6PD | Yes | Severe | Urosepsis (Citrobacter) |
L-090 | 1996 | 3210 | 39 | m/W | 2.0 | 7.0 | 47.9 | 47.9 | Advanced | Yes | Yes | Galactosemia | Yes | Severe | 15% wt loss at day 7 |
C-091 | 1996 | 2808 | 39 | m/B | 2.0 | 8.0 | 30.0 | 30.0 | Moderate | Yes | Yes | G6PD | Yes | None | Cephalohematoma |
M-092 | 1987 | 2700 | 36.5 | m/B | 2.0 | 8.0 | 32.0 | 35.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | ABO Coombs neg, Hct 47% |
L-093 | 1992 | unk | 39 | unk/W | 2.0 | 8.0 | 49.4 | 49.4 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Persistent incr. signals in globus pallidus on multiple MRI <1 year age |
M-094 | 1992 | 3050 | 38 | f/W | 2.0 | 10.0 | 49.4 | 49.4 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | ABO, Coombs neg, Hct 23% |
C-095 | 1997 | 3415 | 39 | m/W | 2.0 | 11.5 | 21.6 | 21.6 | Advanced | No | Yes | Infection | Yes | Severe | Clostridium sepsis, >20% wt loss at day 11.5, Na 166 mEq/l, ABO Coombs neg |
M-096 | 1992 | 3175 | 35 | m/H | 2.0 | 14.0 | 29.4 | 32.7 | Moderate | Yes | Yes | Birth trauma | Yes | Severe | Hct 51% |
P-097 | 2000 | 3320 | 35.7 | f/W | 2.0 | None | not done | None | Subtle | No | No | Idiopathic | Yes | Severe | Prolonged marked jaundice (>6weeks) |
P-098 | 2001 | 4075 | 39 | m/W | 2.0 | None | Not done | Unk | Moderate | No | No | Idiopathic | Yes | Severe | Prolonged jaundiced (>8 weeks), TSB 20 done and recorded at day 4. |
M-099 | 2001 | 3487 | 39 | m/B | 2.5 | 4.0 | 41.4 | 41.4 | Advanced | Yes | Yes | G6PD | Yes | Severe | Hct 42%, no sepsis |
P/M-100 | 1992 | 3289 | 39 | f/W | 2.5 | 4.5 | 23.8 | 23.8 | Advanced | No | Yes | Birth trauma | Yes | Severe | 20% wt loss at day 4.5, Hct 50% |
M-101 | 2000 | 3346 | 36.5 | m/W | 2.5 | 5.0 | 39.5 | 39.5 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | 16% wt loss at day 5 |
C-102 | 1994 | 3025 | 36 | f/W | 2.5 | 5.5 | 36.0 | 36.0 | Subtle | Yes | Yes | Idiopathic | Yes | Severe | 15% wt loss at day 5.5 |
P-103 | 1993 | 3062 | 37 | m/A | 2.5 | 7.0 | 31.4 | 31.4 | Advanced | Yes | Yes | G6PD | Yes | Severe | Birth trauma, 15% wt. loss at day 7, Na 161 mEq/l |
P-104 | 1989 | 3260 | 38.5 | m/W | 2.5 | 7.0 | 40.0 | 40.0 | Advanced | Yes | Yes | Birth trauma | Yes | Severe | Jaundice <24 hours age |
P-105 | 1987 | 2977 | 40 | m/W | 2.5 | 9.0 | 24.5 | 24.5 | Advanced | No | Yes | Idiopathic | Yes | Severe | Hct 56%, TSB at day 8.5 was 23.5 mg/dl |
P-106 | 1998 | 4309 | 38 | m/W | 2.5 | 12.5 | 29.3 | 29.3 | Moderate | No | Yes | Hemolysis | Yes | Severe | ABO Coombs neg, Hct 43%, jaundice < 24 hours |
C-107 | 1993 | 3296 | 38 | m/W | 2.5 | 15.0 | 28.9 | 28.9 | Advanced | No | Yes | Idiopathic | Yes | Severe | Weak suck, arching (age 1 week) |
P-108 | 1998 | 3757 | 36 | m/W | 3.0 | 5.0 | 30.0 | 30.0 | Subtle | No | Yes | Birth trauma | Yes | Moderate | Prolonged jaundiced (>6 weeks) |
L-109 | 1985 | 3771 | 37 | m/W | 3.0 | 5.0 | 39.0 | 39.0 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | >20% wt loss at day 5, Hct 70% |
C-110 | 2002 | unk | 39 | m/B | 3.0 | 6.0 | 39.0 | 39.0 | Moderate | Yes | Yes | Infection | Yes | Moderate | Probable urosepsis |
M-111 | 1993 | 2905 | 36 | f/B | 3.0 | 6.0 | 43.0 | 43.0 | Advanced | Yes | Yes | Hemolysis | Yes | Severe | Hct 36%, abnormal RBC morphology |
L-112 | 1979 | 2820 | 37 | m/W | 3.0 | 7.0 | 49.7 | 49.7 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | 11% wt loss at day 7, Hct 50% |
P-113 | 1999 | 3348 | 39 | f/W | 3.0 | 10.0 | 24.0 | 24.0 | Moderate | No | Yes | Idiopathic | Yes | Moderate | Prolonged jaundiced >4 weeks |
L-114 | 1989 | 4280 | 39 | m/W | 3.0 | 10.0 | 40.3 | 40.3 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | Hct 49% |
P-115 | 1994 | 3632 | 39.5 | m/W | 3.0 | None | None | None | Moderate | No | No | Idiopathic | Yes | Moderate | Jaundice >8weeks, peak TSB unk |
M-116 | 1986 | 2977 | 37 | f/W | 3.5 | 16.0 | 20.7 | 20.7 | Moderate | No | Yes | Idiopathic | Yes | Moderate | Plethora |
C-117 | 1987 | 3250 | 39 | f/W | 4.0 | 8.0 | 41.0 | 41.0 | Moderate | Yes | Yes | Birth trauma | No | Moderate | Hct 40% |
P-118 | 1994 | 2325 | 38 | m/W | 4.0 | None | None | None | Moderate | No | No | Idiopathic | Yes | Moderate | 12% wt loss at day 4 |
C-119 | 2000 | 2977 | 37 | m/B | 6.0 | 13.0 | 54.0 | 54.0 | Advanced | Yes | Yes | G6PD | Yes | Severe | 10.5% wt loss at day 13 |
C-120 | 1999 | 3700 | 38 | m/W | HB | 3.0 | 41.3 | 41.3 | Advanced | Yes | Yes | Crigler-Najjar | Lost | Severe | ABO Coombs neg, abnormal RBC morphology, Hct 66%, Na 149 mEq/l |
C-121 | 1998 | Unk | Unk | m/W | HB | 5.0 | 40.0 | 40.0 | Advanced | Yes | Yes | Crigler-Najjar | Lost | Severe | Follow-up incomplete. |
C-122 | 1999 | 4730 | 39 | m/W | HB | 6.0 | 24.0 | 24.0 | Advanced | Yes | Yes | Infection | Yes | Severe | Home birth Shoulder dystocia; sepsis (E. coli), renal abscess. |
L-123 | 1990 | 4026 | 37 | f/W | HB | 7.0 | 44.7 | 44.7 | Advanced | Yes | Yes | Idiopathic | Yes | Severe | 20% wt loss at day 7, Hct 54% |
C-124 | 2002 | 3632 | 42.5 | f/W | HB | 27.0 | 28.1 | 28.1 | Moderate | No | Yes | Hemolysis | No | Severe | Cong Spherocytosis, Hct 27% |
C-125 | 1992 | 2500 | 36.5 | f/B | None | 8.0 | 42.0 | 46.0 | Advanced | Yes | Yes | G6PD | Yes | Severe | Family history of jaundice, 2 sibs had ExTx |