Table 2 Clinicogenetic classification (consensus 2010)2

From: Inherited ichthyoses/generalized Mendelian disorders of cornification

Non-syndromic ichthyoses

 1. Common ichthyoses

 2. ARCI

 3. KI

 4. Other forms of non-syndromic ichthyosis

Syndromic ichthyoses

 5. X-linked ichthyosis syndromes

 6. Other ichthyosis syndromes (CNS signs, fatal disease course, hair abnormalities and/or other associated signs)

  1. Abbreviations: ARCI, autosomal recessive congenital ichthyosis; CNS, central nervous system; KI, keratinopathic ichthyoses.
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