Fig. 1

Three-generation pedigree of the family indicating individuals affected with autosomal dominant polycystic kidney disease (ADPKD) as a result of a novel missense mutation (R322Q) of the PKD2 gene, as well as those affected with tuberous sclerosis complex (TSC) as a result of a four base-pair deletion (AACA at 2509-2512) of the TSC1 gene. Individual III-5 is the proband (arrow) originally enrolled in our TSC study. Individuals with ? were not available for analyses.