Table 1 The laboratory features of patients with mycosis fungoides/Sézary syndrome analyzed by flow cytometry for T-cell receptor Vβ expression
Patients (N=88) | |
---|---|
Median age (range) | 62 (16–94) |
Sex (male/female) | 49/39 |
Median WBC/μl (range) | 11 813 (3000–67 000) |
Lymphocyte %, median (range) | 34% (2–89%) |
Absolute count/μl, median (range) | 5,111 (196–59 630) |
CD3+CD4+ lymphocyte %, median (range) | 72% (1–99%) |
Absolute count/μl, median (range) | 4,160 (12–57 792) |
SS cells by morphology (mean, range) | |
Cases with ≤5% | 56 (0.6%, 0–5%) |
6–19% | 15 (13%, 6–18%) |
≥20% | 17 (47%, 20–95%) |
Aberrant T-cell phenotype (altered CD2, CD3, CD4, CD5 expression levels) | |
Normal | 57 (65% of cases) |
Abnormal | 31 (35%) |
CD4+CD7− cells | |
Normal (<40% of lymphocytes) | 52 (59%) |
Abnormal (≥40% of lymphocytes) | 36 (41%) |
CD4+CD26− cells | |
Normal (<35% of lymphocytes) | 26 (30% of cases) |
Abnormal (≥35% of lymphocytes) | 62 (70%) |
CD4/CD8 ratio | |
<10 | 49 (56% of cases) |
≥10 | 39 (44%) |
Flow cytometric Vβ analysis | |
Negative | 22 (25% of cases) |
Positive | 66 (75%) |
Single Vβ+ | 44 (50%) |
≥70% Non-reactive | 22 (25%) |
Molecular clonality analysis | |
Positive | 28 (70% of tested cases) |
Oligoclonal | 4 (10%) |
Negative | 8 (20%) |
Not performed | 47 |