Table 1 Clinicopathological features and follow-up
From: Anaplastic sarcomas of the kidney are characterized by DICER1 mutations
ASK | Age/sex | Side | Notable gross pathological finding | Initial pathological diagnosis | Stage | Treatment | Follow-up | Outcome |
|---|---|---|---|---|---|---|---|---|
1 | 36 mo/F | L | D=15 cm | Anaplastic Wilms tumor | I | N+CHT | No recurrence | NED 14 yrs |
2 | 120 mo/M | L | D=17 cm; W=1210 g; nodular mass protruding into renal pelvis | Sarcomatoid variant of renal cell carcinoma | I | N+CHT | No recurrence | NED 8 yrs |
3 | 139 mo/M | R | D=8 cm; W=296 g solid; intra-pelvic growth | Anaplastic Wilms tumor | II | CHT+N+CHT | Unknown | Unknown |
4 | 106 mo/F | L | D=5 cm; W=224 g; 2/3 cystic | Anaplastic Wilms tumor vs ASK | I | N+CHT | Unknown | Unknown |
5 | 18 mo/M | R | D=28 cm; W=3400 g; solid/cystic mass | Anaplastic Wilms tumor | III | CHT+N+CHT | Unknown | Unknown |
6 | 18 mo/M | R | D=10 cm; W=670 g; solid/cystic mass protruding into renal pelvis | Anaplastic Wilms tumor | I | N+CHT | No recurrence | NED 13 yrs |
7 | 10 mo/F or 105 mo/F | L | ASK D=12.9 cm | Renal cysts identified at 10 mo Anaplastic sarcoma of the kidney at 105 mo | III | R+CHT | No recurrence | NED 12 yrs |
8 | 156 mo/M | R | D=16 cm; W=666 g | Anaplastic Wilms tumor | III | CHT+R | Recurrence of 3 cm mass in right upper retroperitoneum | DOD 5 mo |
9 | 7 mo/F | L | D=18 cm; W=1620 g; cystic mass | Anaplastic sarcoma of the kidney | I | N | No recurrence | NED 2 yrs |
