Table 1 Patients and cell characteristics
Fibroblasts | Age at biopsy | Race | Phenotype | Clinical characteristics | Onset of tumors |
---|---|---|---|---|---|
FMD | 16 years | Caucasian | NA | NA | NA |
FH29 | 30 years | Caucasian | NA | NA | NA |
FH84 | 28 years | Black | NA | NA | NA |
XP148 | 12 years | Caucasian | XP-C | Multiple BCCs and SCCs, face and exposed areas | 9 years |
XP188VI | 7 years | Caucasian | XP-C | Several SCC and 1 BCC on the face | ND |
XP373VI | 4 years | Caucasian | XP-C | 1 facial BCC | 2 years |
XP424VI | 17 years | Caucasian | XP-C | 3 facial BCC, several pigmented lesions (ephelides, naevus) | 17 years |
XP433VI | 2 months | Caucasian | XP-C | NA | NA |
XP521VI | 29 years | Black | XP-C | Photophoby. SCC of the lip. Multiple lentigines. Small eye carcinomas | 14 years |