Table 2 Mastocytosis types and subtypes.
Cutaneous mastocytosis |
Urticaria pigmentosa/Maculopapular cutaneous mastocytosis |
Monomorphic |
Polymorphic |
Diffuse cutaneous mastocytosis |
Cutaneous mastocytoma |
Isolated mastocytoma |
Multilocalized mastocytoma |
Systemic mastocytosis |
Bone marrow mastocytosis |
Indolent systemic mastocytosis |
Smoldering systemic mastocytosis |
Aggressive systemic mastocytosis |
Systemic mastocytosis with an associated haematologic neoplasm |
Mast cell leukemia |
Mast cell sarcoma |