Table 1 Clinical and laboratory findings in 23 patients with hairy cell leukemia-variant
Casec | Agea, (y) Sex | Examined organ sites | Initial clinical presentation | Splenomegaly, g or cm below costal margin | Hepatomegaly | LAD | Other organ involvment | WBC ×109/L | HGB (g/dL) | PLT x 109/L | Mo ×109/L | Ly x 109/L |
---|---|---|---|---|---|---|---|---|---|---|---|---|
1 | 65 F | BM | NA | Yesb | No | Yes, diaphragmatic | No | 41.7 | 13 | 202 | 0.8 | 36.7 |
2 | 77 F | BM | Thrombocytopenia | No | No | NA | NA | 47 | 12.6 | 21 | 9.0 | 27.2 |
3 | 69 M | BM Brain | WBC elevation on routine exam | Yesb | No | No | Brain | 74 | 11.6 | 92 | 0.7 | 72 |
4 | 63 M | BM Spleen Liver LN | WBC elevation B-symptoms LAD | Yes, 2690 g | Yes | Yes, axillary, gastric, periportal, mesenteric | Liver LN Terminal ileumc | 72 | 13.8 | 140 | 10.8 | 61.9 |
5 | 80 F | BM | Abdominal pain Thrombocytopenia | Yesb | Yes | Yes, abdominal | No | 14.4 | 12.7 | 79 | 0.1 | 9.9 |
6 | 50 M | BM Spleen Liver Omentum | Bruising (low Plt) WBC elevation | Yes, 4500 g | Yes | No | Liver Omentum | 56.1 | 8 | 121 | 3.9 | 49.4 |
7 | 70 M | BM | WBC elevation on routine exam | Yes, 16 cm | No | No | No | 38.6 | 16.2 | 130 | 1.5 | 27.02 |
8 | 70 M | BM | Incidental finding on PB evaluation for PMF, Night sweats Anemia | Yes, 25 cm | No | No | No | 8.5 | 9.1 | 295 | 0.3 | 6.9 |
9 | 64 M | BM | WBC elevation during evaluation for Melanoma | Yesb | No | Yes, retroperitoneal | No | 23.3 | 15.4 | 127 | 0.2 | 19.8 |
10 | 56 M | BM | WBC elevation on routine exam | No | No | No | No | 15.4 | 15.9 | 240 | 0.5 | 6.9 |
11 | 89 F | BM | B-symptoms Thrombocytopenia | Yes, 10 cm | No | No | No | 5.7 | 11.5 | 137 | 0.2 | 3.2 |
12 | 75 M | BM | WBC elevation on routine exam | Yes, 7 cm | Yes | No | No | 67.2 | 10 | 154 | 1.3 | 44.3 |
13 | 50 M | BM | Abdominal pain WBC elevation | Yes | No | NA | No | 12.9 | 6.7 | 24 | 0.6 | 6. 5 |
14 | 52 M | BM | WBC elevation Thrombocytopenia on routine physical | Yesb | No | No | No | 21.4 | 15.4 | 122 | 1.1 | 6.6 |
15 | 70 M | BM | WBC elevation on evaluation for repeated falls | Yes, 35 cm | No | No | No | 45.9 | 8.4 | 60 | 0.4 | 41.3 |
16 | 79 F | BM | Abdominal pain Cytopenias | Yes, 10 cm | No | No | No | 20.9 | 11.4 | 104 | 0.2 | 16.7 |
17 | 72 F | BM Spleen | Abdominal pain | Yes, 2240 g | NA | No | No | NA | NA | NA | NA | NA |
18 | 80 M | BM | NA | Yes Splenectomy | NA | NA | Skinc | 56.9 | 10.9 | 39 | NA | 39.8 |
19 | 77 M | BM Spleen Liver | NA | Yes, 1740g | NA | NA | Liver | 5.4 | 10.7 | 96 | NA | 3.6 |
20 | 64 F | BM | Fatigue Thrombocytopenia | NA | NA | NA | NA | 4.5 | 13.2 | 44 | 0.4 | 1.8 |
21 | 83 M | BM | Cytopenias | NA | NA | NA | NA | 22 | 12.6 | 53 | 0.6 | 17.4 |
22 | 84 M | BM LN | Abdominal pain Cytopenias | Yesb | No | Yes, Retroperitoneal, portocaval | LN | 4.2 | 8.8 | 79 | 0.2 | 1.3 |
23 | 75 M | BM | Fatigue Thrombocytopenia | Yes, 7 cm | Yes | Yes, cervical | No | 55.6 | 14.1 | 79 | 2.2 | 50.6 |