Table 1 Clinical and laboratory findings in 23 patients with hairy cell leukemia-variant

From: Clinicopathologic and molecular features in hairy cell leukemia-variant: single institutional experience

Casec

Agea, (y) Sex

Examined organ sites

Initial clinical presentation

Splenomegaly, g or cm below costal margin

Hepatomegaly

LAD

Other organ involvment

WBC ×109/L

HGB (g/dL)

PLT x 109/L

Mo ×109/L

Ly x 109/L

1

65 F

BM

NA

Yesb

No

Yes, diaphragmatic

No

41.7

13

202

0.8

36.7

2

77 F

BM

Thrombocytopenia

No

No

NA

NA

47

12.6

21

9.0

27.2

3

69 M

BM

Brain

WBC elevation on routine exam

Yesb

No

No

Brain

74

11.6

92

0.7

72

4

63 M

BM

Spleen

Liver

LN

WBC elevation

B-symptoms

LAD

Yes, 2690 g

Yes

Yes, axillary, gastric, periportal, mesenteric

Liver

LN

Terminal ileumc

72

13.8

140

10.8

61.9

5

80 F

BM

Abdominal pain Thrombocytopenia

Yesb

Yes

Yes, abdominal

No

14.4

12.7

79

0.1

9.9

6

50 M

BM

Spleen

Liver

Omentum

Bruising (low Plt)

WBC elevation

Yes, 4500 g

Yes

No

Liver

Omentum

56.1

8

121

3.9

49.4

7

70 M

BM

WBC elevation on routine exam

Yes, 16 cm

No

No

No

38.6

16.2

130

1.5

27.02

8

70 M

BM

Incidental finding on PB evaluation for PMF, Night sweats

Anemia

Yes, 25 cm

No

No

No

8.5

9.1

295

0.3

6.9

9

64 M

BM

WBC elevation during evaluation for Melanoma

Yesb

No

Yes, retroperitoneal

No

23.3

15.4

127

0.2

19.8

10

56 M

BM

WBC elevation on routine exam

No

No

No

No

15.4

15.9

240

0.5

6.9

11

89 F

BM

B-symptoms

Thrombocytopenia

Yes, 10 cm

No

No

No

5.7

11.5

137

0.2

3.2

12

75 M

BM

WBC elevation on routine exam

Yes, 7 cm

Yes

No

No

67.2

10

154

1.3

44.3

13

50 M

BM

Abdominal pain

WBC elevation

Yes

No

NA

No

12.9

6.7

24

0.6

6. 5

14

52 M

BM

WBC elevation

Thrombocytopenia on routine physical

Yesb

No

No

No

21.4

15.4

122

1.1

6.6

15

70 M

BM

WBC elevation on evaluation for repeated falls

Yes, 35 cm

No

No

No

45.9

8.4

60

0.4

41.3

16

79 F

BM

Abdominal pain Cytopenias

Yes, 10 cm

No

No

No

20.9

11.4

104

0.2

16.7

17

72 F

BM

Spleen

Abdominal pain

Yes, 2240 g

NA

No

No

NA

NA

NA

NA

NA

18

80 M

BM

NA

Yes Splenectomy

NA

NA

Skinc

56.9

10.9

39

NA

39.8

19

77 M

BM

Spleen

Liver

NA

Yes, 1740g

NA

NA

Liver

5.4

10.7

96

NA

3.6

20

64 F

BM

Fatigue

Thrombocytopenia

NA

NA

NA

NA

4.5

13.2

44

0.4

1.8

21

83 M

BM

Cytopenias

NA

NA

NA

NA

22

12.6

53

0.6

17.4

22

84 M

BM

LN

Abdominal pain Cytopenias

Yesb

No

Yes, Retroperitoneal, portocaval

LN

4.2

8.8

79

0.2

1.3

23

75 M

BM

Fatigue

Thrombocytopenia

Yes, 7 cm

Yes

Yes, cervical

No

55.6

14.1

79

2.2

50.6

  1. F female, HGB hemoglobin, LAD lymphadenopathy, Ly lymphocytes, M male, Mo monocytes, NA not available, PLT platelets, WBC white blood cells, y years
  2. aAge indicates age at initial diagnosis
  3. bSplenomegaly by imaging studies
  4. cReported from the outside institution