Fig. 6

Fibrosarcomatous dermatofibrosarcoma protuberans. a The tumor shows a fascicular fibrosarcoma-like architecture and contains elongated spindle cells with vesicular chromatin. b “Myoid nodules” are sometimes seen in dermatofibrosarcoma protuberans, most often in the fibrosarcomatous variant. c Lung metastases can be challenging to diagnosis without clinical history. d Fluorescence in situ hybridization (FISH) for PDGFB is a helpful diagnostic adjunct. Note the isolated 3’ (centromeric) signals, which are multiple in this case