Abstract
Introduction
Ewing’s sarcoma is a Primary Neuroectodermal Tumour (PNET) commonly affecting appendicular skeleton. The involvement of axial skeleton is very rare and that too of cervical spine is rarest. We present a case of Ewing’s sarcoma involving cervical spine managed surgically, and its outcome.
Case presentation
A 26-year-old male presented with 3-month history of neck pain and progressive motor weakness for 1 week. After clinical evaluation of sign and symptoms, MRI of cervical spine revealed a posterior neck mass over C2, C3 and C4. Because of mass effect and spinal cord compression, early surgical intervention was deemed necessary to stop progression of neurological deficit and make tissue diagnosis of lesion. On histopathological examination diagnosis of Ewing sarcoma was made. PET-CT showed C2 and C3 as primary site of involvement with no other site of involvement.
Discussion
The Ewing’s Sarcoma of the cervical spine is a rare occurrence and usually present in late and advanced stage. High index of suspicion should be present to make early diagnosis and prevent complications.
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Data availability
The datasets generated during and/or analysed during the current study are available from the corresponding author on reasonable request.
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MNA observed and wrote the case presentation for the manuscript. AG wrote rest of the manuscript and was responsible for revision. DKJ proofread the manuscript. DR was responsible for reviewing the case slides and confirmation of diagnosis.
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Ansari, M.N., Gupta, A., Jain, D.K. et al. The Ewing's sarcoma of cervical spine—a rare occurrence. Spinal Cord Ser Cases 8, 68 (2022). https://doi.org/10.1038/s41394-022-00534-6
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DOI: https://doi.org/10.1038/s41394-022-00534-6
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