Table 2 List of genes involved in complement activation and complement receptor activity.

From: Inhibition of the immunoproteasome modulates innate immunity to ameliorate muscle pathology of dysferlin-deficient BlAJ mice

ENSEMBL ID

Symbol

Name

log2FoldChange

p value

Upregulated genes in 6m BlAJ mouse

  

ENSMUSG00000098470

C1rb

Complement Component 1, R Subcomponent B

8.182263074

0.001250885

ENSMUSG00000079343

C1s2

Complement Component 1, S Subcomponent 2

5.587182004

0.000871793

ENSMUSG00000023992

Trem2

Triggering Receptor Expressed On Myeloid Cells 2

0.733157851

0.096146313

ENSMUSG00000022887

Masp1

Mannan-Binding Lectin Serine Peptidase 1

0.69300433

0.014662732

ENSMUSG00000073418

C4b

Complement Component 4B (Chido Blood Group)

0.533914616

0.140061036

ENSMUSG00000022018

Rgcc

Regulator Of Cell Cycle

0.49190354

0.019297844

ENSMUSG00000074361

C5ar2

Complement Component 5A Receptor 2

0.401272021

0.519986508

ENSMUSG00000024164

C3

Complement Component 3

0.295320134

0.346800669

ENSMUSG00000032679

Cd59a

Cd59A Antigen

0.285061323

0.125542455

ENSMUSG00000018446

C1qbp

Complement Component 1, Q Subcomponent Binding Protein

0.227746982

0.16028519

ENSMUSG00000036905

C1qb

Complement Component 1, Q Subcomponent, Beta Polypeptide

0.220271038

0.391784631

ENSMUSG00000038845

Phb

Prohibitin

0.213011255

0.187137225

ENSMUSG00000049130

C5ar1

Complement Component 5A Receptor 1

0.201042989

0.598542063

ENSMUSG00000036887

C1qa

Complement Component 1, Q Subcomponent, Alpha Polypeptide

0.16729138

0.520117499

ENSMUSG00000042436

Mfap4

Microfibrillar-Associated Protein 4

0.145458769

0.659127548

ENSMUSG00000036896

C1qc

Complement Component 1, Q Subcomponent, C Chain

0.140524774

0.583171884

ENSMUSG00000001128

Cfp

Complement Factor Properdin

0.090370496

0.776127139

ENSMUSG00000024371

C2

Complement Component 2 (Within H-2S)

0.062776152

0.881526526

ENSMUSG00000015083

C8g

Complement Component 8, Gamma Polypeptide

0.06103822

0.847147746

Upregulated genes in 12m BlAJ mouse

  

ENSMUSG00000038521

C1s1

Complement Component 1, S Subcomponent 1

–0.115238369

0.86477287

ENSMUSG00000040552

C3ar1

Complement Component 3A Receptor 1

–0.153607904

0.684275666

ENSMUSG00000055172

C1ra

Complement Component 1, R Subcomponent A

–0.175069968

0.559598517

ENSMUSG00000016493

Cd46

Cd46 Antigen, Complement Regulatory Protein

–0.222483616

0.663841819

ENSMUSG00000042190

Cmklr1

Chemokine-Like Receptor 1

–0.253811222

0.169253436

ENSMUSG00000026399

Cd55

Cd55 Molecule, Decay Accelerating Factor For Complement

–0.292896576

0.067893029

ENSMUSG00000016481

Cr1l

Complement Component (3B/4B) Receptor 1-Like

–0.297021748

0.168692966

ENSMUSG00000016481

Cr1l

Complement Component (3B/4B) Receptor 1-Like

–0.297021748

0.168692966

ENSMUSG00000026938

Fcna

Ficolin A

–0.339976874

0.492867204

ENSMUSG00000023224

Serping1

Serine (Or Cysteine) Peptidase Inhibitor, Clade G, Member 1

–0.380740967

0.143743832

ENSMUSG00000061780

Cfd

Complement Factor D (Adipsin)

–0.519289828

0.110160899

ENSMUSG00000038527

C1rl

Complement Component 1, R Subcomponent-Like

–0.794072347

0.165929881

ENSMUSG00000026365

Cfh

Complement Component Factor H

–1.381019074

0.000280545

ENSMUSG00000079105

C7

Complement Component 7

–2.282311274

0.003259106