Table 1 Characteristics and complications of individuals with a clinical and molecular diagnosis of vEDS in childhood.

Median age at last follow up in childhood

11(7–16)

12 (6–15)

11 (8–17

–

9 (6–17)

13 (8–16)

–

Median age at molecular diagnosis

7 (2–13)

6 (2–13)

7 (3–12)

ns

7 (2-13)

7 (3–13)

ns

≥1 event in childhood

13 (21%)

4 (13%)

9 (27%)

ns

8 (35%)

5 (13%)

0.05

Median age at first event

11 (0–13)

6 (0–12)

11 (0–15)

ns

13 (8–14)

0 (0–9)

ns

≥1 vascular event in childhood

2 (3%)

1 (3%)

1 (3%)

ns

2 (9%)

0 (0%)

ns

≥1 gastrointestinal event in childhood

6 (10%)

1 (3%)

5 (15%)

ns

4 (17%)

2 (5%)

ns

≥1 other organ rupture in childhood^a

6 (10%)

2 (7%)

4 (12%)

ns

3 (13%)

3 (8%)

ns