Table 3 Minor diagnostic criteria (2017 international classification of the Ehlers-Danlos syndromes criteria).

≥1 minor criteria present

56 (93%)^a

27 (96%)^a

29 (91%)^a

ns

21 (95%)

35 (92%)^a

ns

Median number of minor criteria

3 (2–4)

3 (2–3)

3 (2–4)

ns

3 (2.5–4)

3 (2–3)

ns

Excessive bruising

51 (82%)^a

26 (87%)

25 (78%)^a

ns

19 (83%)

32 (82%)^a

ns

Thin translucent skin

42 (76%)^a

22 (79%)^a

20 (74%)^a

ns

18 (81%)^a

24 (73%)^a

ns

Characteristic facial appearance^b

28 (57%)^a

13 (57%)^a

15 (58%)^a

ns

14 (70%)^a

14 (48%)^a

ns

Spontaneous pneumothorax

5 (8%)

1 (3%)

4 (12%)

ns

2 (8%)

3 (7%)

ns

Acrogeria

3 (5%)

1 (3%)

2 (6%)

ns

2 (8%)

1 (2%)

ns

Talipes equinovarus

7 (11%)

5 (17%)

2 (6%)

ns

2 (8%)

5 (12%)

ns

Congenital hip dislocation

1 (2%)

1 (3%)

0 (0%)

ns

1 (4%)

0 (0%)

ns

Hypermobility of small joints

40 (87%)^a

18 (82%)^a

22 (92%)^a

ns

17 (94%)^a

23 (82%)^a

ns

Tendon rupture

3 (5%)

1 (3%)

2 (6%)

ns

0 (0%)

3 (8%)

ns

Gingival recession and fragility

9 (27%)^a

6 (35%)^a

3 (19%)^a

ns

4 (27%)^a

5 (28%)^a

ns

Early onset varicose veins

1 (2%)

0 (0%)

1 (3%)

ns

1 (4%)

0 (0%)

ns