Fig. 5: Forest plot for effect of delayed emergency treatment (ET) on development of acute onset movement disorder (MD) in patients identified by newborn screening (NBS) including and excluding noninformative studies.

Patients with delayed ET show an increased relative risk (log risk ratio) for development of an acute onset MD compared with patients with adequate ET (p < 0.0001). The relative risk increases further if noninformative studies are excluded (p < 0.0001). CI confidence interval, RE random effect. Including noninformative studies: test of heterogeneity: QM(df = 9) = 6.26, p = 0.7132; model results: p < 0.0001. I2 (residual heterogeneity/unaccounted variability): 0%. Excluding noninformative studies: test of heterogeneity QM(df = 3) = 2.1756, p = 0.5368; model results: p < 0.0001. I2 (residual heterogeneity/unaccounted variability): 0%.