Table 1 Heart defects and surgeries.

From: HVSMR-2.0: A 3D cardiovascular MR dataset for whole-heart segmentation in congenital heart disease

 

Description

Count

Percentage

Mild

 

12

20%

~Normal

Left: LA ↔ LV ↔ AO, Right: SVC/IVC ↔ RA ↔ RV ↔ PA

8

13%

Mild/Moderate Dilation

A chamber and/or vessel is mildly or moderately dilated

4

7%

Moderate

 

11

18%

VSD

Hole in the septal wall between the two ventricles

29

48%

ASD

Hole in the septal wall between the two atria

23

38%

DORV

AO ↔ RV and PA ↔ RV, always with VSD

22

37%

D-Loop TGA

AO ↔ RV and PA ↔ LV, with switched vessels

7

12%

S/P Arterial Switch for TGA

AO and PA are cut and reattached to the correct ventricle

1

2%

Bilateral SVC

Two SVCs, one on each side of the heart

9

15%

Severe Dilation

A chamber and/or vessel is severely dilated

4

7%

Tortuous Vessels

Vessels have abnormal twists and turns, due to arterial tortuousity syndrome or giant collaterals

2

3%

Severe

 

37

62%

Dextrocardia

Heart points to the right side

10

17%

Mesocardia

Heart points to the midline

4

7%

Inverted Ventricles

Labeled LV on right side of the body, labeled RV on left side

15

25%

Inverted Atria

Labeled LA on right side of the body, labeled RA on left side

7

12%

Left/Central IVC

IVC positioned on the left side or centrally

16

27%

Left/Central SVC

A single SVC positioned on the left side or centrally

6

10%

L-Loop TGA

AO ↔ RV and PA ↔ LV, with switched ventricles

3

5%

S/P Atrial Switch for TGA

Baffle connects SVC ↔ LV and IVC ↔ LV; return from pulmonary veins ↔ RV, AO ↔ RV and PA ↔ LV remain

1

2%

S/P Rastelli Procedure

Septal defect is patched; implanted baffle connects PA ↔ RV

2

3%

Single Ventricle

One ventricle, with any morphology, labeled as LV

6

10%

DILV

Large LV, small RV, AO ↔ LV, PA ↔ LV

4

7%

DI-DORV

Both atrioventricular valves ↔ RV, AO ↔ RV, PA ↔ RV

1

2%

Common Atrium

One atrium, labeled as LA

10

17%

S/P Glenn Procedure

SVC ↔ PA

24

40%

S/P Fontan Procedure

IVC ↔ PA, always S/P Glenn procedure

9

15%

Coincident Variants

   

Heterotaxy

Abnormal left/right arrangement of the heart or other organs

13

22%

Superoinferior Ventricles

Ventricles sit one above the other

3

5%

PA Atresia or MPA Stump

Pulmonary valve is poorly developed or surgically closed

9

15%

S/P PA Banding

Implanted band to narrow the main PA trunk

7

12%

AO-PA Anastomosis

Damus-Kaye-Stansel anastomosis (proximal PA sewn to aorta)

4

7%

Marfan Syndrome

Connective tissue disorder, can cause abnormal chest anatomy

3

5%

CMR Artifact (AO)

Dark artifact in the AO

9

15%

CMR Artifact (PA)

Dark artifact in the PA

13

22%

  1. Subjects can have multiple diagnoses, and are categorized as “mild”, “moderate” or “severe” according to the most serious defect in the case. Coincident variants are not used to categorize subjects. Prior conditions that have been previously corrected such that they are no longer visible in the scan are not included. However, hearts with multiple defects may deviate in anatomy from the descriptions below (e.g., patients with DORV who are S/P Glenn procedure have SVC ↔ PA and not PA ↔ RV). A dilated chamber or vessel is only noted if it is the sole diagnosis. The ↔ symbol indicates that two structures are connected, with blood flow between them. VSD = ventricular septal defect, ASD = atrial septal defect, DORV = double outlet right ventricle, TGA = transposition of the great arteries, DILV = double inlet left ventricle, DI-DORV = double inlet-double outlet right ventricle, S/P = status post (previous surgery).