Table 2 The comparisons between dietary intake and growth and body composition in PKU patients.

From: Dietary intake and nutritional status of patients with phenylketonuria in Taiwan

Subject characteristics

PKU patients

p-value

Phe-free formula (N = 12)

Non-Phe-free formula (N = 10)

Age years ± SD

15.75 ± 5.92

14.60 ± 4.48

0.69

Growth

Height z scoreb

− 0.839 ± 2.201

− 0.694 ± 1.755

0.7713

Weight z scoreb

− 0.623 ± 1.403

− 0.597 ± 1.426

0.9474

BMI z scoreb

− 0.318 ± 1.511

− 0.43 ± 1.062

0.4097

Body composition

Muscle mass (%)

73.15 ± 8.5

73.68 ± 9.5579

0.9474

Fat mass (%)

20.975 ± 8.603

20.46 ± 9.705

0.9229

Dietary intake

Natural protein, g/kg/day

0.574 ± 0.316

1.234 ± 0.679

0.004

Total protein, g/kg/day

1.292 ± 0.54

1.233 ± 0.678

0.7223

Energy intake, g/kg/day

42.279 ± 16.159

41.466 ± 14.518

0.9742

Protein intake of DRIs (%)

109.672 ± 28.606

100.379 ± 39.395

0.5824

Energy intake of DRIs (%)

106.142 ± 21.289

100.361 ± 23.75

0.5387

  1. ap-values were calculated using Mann–Whitney U test.
  2. bZ-scores = (raw score-the mean of the controls)/the standard deviation of the controls.