Table 1 Patient characteristics.
Patient | Age, years | Sex | Protopathy | Diagnosis time for protopathy | Diagnosis time for thrombocytopenia | Lowest platelet counts(× 109/L) | Previous treatments | Complications | Acompanying diseases | APS | Reticulocytes ratio (%) | Bone marrow puncture | SLEDAI |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|
1 | 54 | F | SLE | 1988 | 2014 | 2 | Pred,CysA, CTX, IVIG, vincristine, transfused platelets | No | Hypertension Diabetes | Yes | 2.14 | NA | 3 |
2 | 54 | F | SLE | 2005 | 2005 | 12 | Pred, CysA | No | HBC,Spleno-megaly, Hyperthyroid-ism | No | NA | NA | |
3 | 31 | F | SLE | 2005 | 2005 | 5 | Pred, CysA, AZA | No | No | No | NA | NA | |
4 | 47 | F | UCTD | 2015 | 2015 | 9 | Pred, CysA | No | No | No | 3.97 | NA | 1 |
5 | 42 | F | SS | 2016 | 2016 | 7 | Pred, HCQ, CysA, IVIG, TPO | No | No | No | 2.74 | AA | |
6 | 37 | F | SLE | 2013 | 2018 | 1 | Pred, HCQ, CysA, MMF, IVIG, splenectomy | Autoimmune hemolytic anemia | No | No | 2.31 | Normal | 1 |
7 | 22 | F | SLE | 2018 | 2018 | 9 | Pred, CysA, TPO | No | No | No | 1.23 | ITP | 5 |
8 | 16 | M | SLE | 2017 | 2017 | 3 | Pred, CysA, IVIG | No | No | No | 2.47 | ITP | 3 |
9 | 40 | F | SLE | 2018 | 2018 | 1 | Pred, HCQ, CysA, IVIG, RTX | PAH | No | No | 5.24 | ITP | 5 |
10 | 53 | F | SS | 2003 | 2003 | 4 | Pred, HCQ, transfused platelets | No | No | No | 3.39 | Megakaryocytopen-ia | |
11 | 63 | M | UCTD | 2019 | 2019 | 3 | Pred, CysA, IVIG, TPO | No | No | No | 1.73 | Normal | |
12 | 54 | F | SS | 2018 | 2018 | 2 | Pred, CysA, IVIG, TPO | No | Ovarian cancer | No | 0.55 | Megakar-yocyte deficiency | |
13 | 27 | F | SLE | 2014 | 2014 | 10 | Pred, CysA, IVIG, CTX, RTX, plasma exchange | No | No | No | 1.76 | MAS | 16 |
14 | 22 | M | UCTD | 2015 | 2015 | 10 | Pred | No | No | No | NA | ITP | |
15 | 47 | F | SLE | 2018 | 2018 | 12 | Pred, CysA | No | No | No | NA | ITP | 1 |