Table 3 Comparison between the largest cohorts of PCNSV.

From: Primary CNS vasculitis (PCNSV): a cohort study

 

Mayo cohort4

French cohort5

Sundaram et al.10

AIIMS cohort

Total cases

163

112

45

82

Median age (years)

48

47

36

28.6

Sex (M:F)

78:89

60:52

31:14

68:14

Most common symptom

Headache (59.5%)

Motor deficit

Hemiparesis

Seizures (70.7%)

Abnormal DSA

113/163 (69.3)

74/95 (78)

30/42 (71)

45/46 (97.8)

Abnormal biopsy (%)

58/81 (72)

33/53 (62)

19/29 (66)

50/56 (89.3)

Abnormal CSF (%)

117/126 (93)

73/104 (70)

25/45 (60)

42/48 (87.5)

Median mRS

 

2

2

2

Good functional outcome

mRS 0–3

mRS 0–2: 63/112

56%

mRS 0–2: 33/45

77%

mRS 0–2: 30/46

65.2%

Mortality (%)

25/163 (15)

9/112 (8)

7/45 (16)

4/46 (8.5%)