Fig. 1

Plasma and brain creatine and creatinine levels are markedly reduced in Slc6a8-/y mice while guanidinoacetic acid is mildly increased. (A) Plasma creatine, (B) brain creatine, (C) plasma creatinine, (D) brain creatinine, (E) plasma guanidinoacetic acid, and (F) brain guandinoacetic acid. All data is presented as mean + standard deviation. P values between 0.0001 and 0.001 are shown with three (***), and P values less than 0.0001 are shown with four (****). (GAA, guanidinoacetic acid)