Table 1 Clinical characteristics of patients with I-DiPO and S-DiPO.
 | Idiopathic (N = 18) | Secondary (N = 7) | Test result P value |
---|---|---|---|
Sex (M:F) | 14:4 | 6:1 | NS |
 Male (M) | 14 (77.8%) | 6 (85.71%) | |
 Female (F) | 4 (22.2%) | 1 (14.29%) | |
Mean age at diagnosis of DiPO | 37.8 (years) | 67.8 (years) | < 0.05 |
Smoking status (N:F) | 16:2 | 5:2 | NS |
 Never (N) | 16 (88.9%) | 5 (71.4%) | |
 Former (F) | 2 (11.1%) | 2 (28.6%) | |
Laboratory data | |||
 ALP (U/L: 80–260) | 218.31 (N = 16) | 259.00 (N = 6) | NS |
 Corrected Ca (mg/dL: 8.4–10.4) | 9.43 (N = 16) | 9.32 (N = 5) | NS |
 P (mg/dL: 2.5–4.5) | 3.20 (N = 13) | 3.60 (N = 1) | NS |
Lung function test | |||
 %FVC | 86.83 (N = 18) | 90.45 (N = 4) | NS |
 %FEV1 | 80.95 (N = 18) | 87.75 (N = 4) | NS |
Family history | 2 (10%) | 0 | Â |
Deterioration of pulmonary ossification on HRCT | (N = 18) | (N = 4) | NS |
 Stable | 2 (11.1%) | 1 (14.29%) | |
 Progression | 13 (72.2%) | 1 (14.29%) | |
 Unknown | 3 (16.7%) | 5 (71.4%) | |
Survival | (N = 18) | (N = 4) | < 0.05 |
 Alive | 16 (88.9%) | 3 (42.9%) | |
 Dead | 0 | 3 (42.9%) | |
 Unknown | 2 (11.1%) | 1 (14.2%) | |
Underlying diseases |  | (N = 4) |  |
 Interstitial pneumonia |  | 5 (71.43%) |  |
 Atrial fibrillation |  | 3 (42.86%) |  |
 Acute respiratory distress syndrome |  | 1 (14.30%) |  |
 Mitral stenosis |  | 1 (14.30%) |  |