Table 1 Respiratory chain enzyme activities.

From: Exercise intolerance and developmental delay associated with a novel mitochondrial ND5 mutation

  

Reference Value (%)

 
 

Activitya (%)

Deficiency

Low

Normal

Result

Complex I

57.2

<64.5

64.5 ~ 76.3

76.3 ~ 161.3

Deficiency

Complex II

139.4

<62.5

62.5 ~ 74.1

74.1 ~ 174.1

Normal

Complex I + III

70.5

<63.0

63.0 ~ 73.1

73.1 ~ 177.8

Low

Complex IV

55.3

<62.3

62.3 ~ 71.9

71.9 ~ 238.0

Deficiency

Complex V

79.9

<60.7

60.7 ~ 75.2

75.2 ~ 566.2

Normal

  1. aactivity was presented as ratio of ( complex enzyme activity/citrate synthase).