Figure 1: Structure of ANG with ALS/PD variants marked.

The active site residues (H13, K40, H114) and the nuclear localization sequence (R31, R32, R33) are shown and are labelled in black along with the N- and C-termini. The disulphide bridges are also shown. K40 and R31 both show multiple conformations. Helices are labelled in dark green and strands in pink. Figures were created using the program PyMOL (http://www.delanoscientific.com)