Figure 1: Assay of TTR tetrameric stability by IEF.

(A) Plasma TTR from heterozygote carriers of TTR variants or from controls were isolated by native PAGE electrophoresis and then separated by IEF in semi-dissociating conditions (4 M urea). This is a representative picture selected from the 3 replicas considered for the quantification presented in (B). (B) Relative abundance of tetramer was calculated based on the ratio of intensity of tetramer bands (% Tetramer) over intensity of all TTR bands (Total TTR) in samples from plasma. *P < 0.05 (Student’s t-test). Error bars indicate SD.