Pulmonary arterial hypertension (PAH) contributes significantly to the morbidity and mortality of patients with systemic sclerosis. Clinical symptoms of PAH are unspecific and are late manifestations of disease. This Case Study highlights the challenges of diagnosing PAH in patients with systemic sclerosis and includes discussion of screening options.
- Jörg HW Distler
- Marius M Hoeper
- Oliver Distler
