Table 1 Stages of angiomyolipomata according to the number of lesions, size and impact on kidney structure

From: Clinical practice recommendations for kidney involvement in tuberous sclerosis complex: a consensus statement by the ERKNet Working Group for Autosomal Dominant Structural Kidney Disorders and the ERA Genes & Kidney Working Group

Stage

Number of lesions

Size

Morphology

0

None

NA

NA

1

1–4

<3 cm

Normal

2

>5

<3 cm

Normal

3

<5

1 lesion >3 cm

Intact

4

>5

2–4 lesions >3 cm

Intact

5

>5

>5 lesions >3 cm

Recognizable

6

>5

1 lesion >5 cm

Not recognizable

  1. NA, not applicable. Table reprinted with permission from ref. 1, Wiley.
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