TABLE 2 Clinical Data for Cases of Pagetoid Reticulosis

From: Pagetoid Reticulosis (Woringer-Kolopp Disease): An Immunophenotypic, Molecular, and Clinicopathologic Study

Case

Age/Sex

Durationa

Location

Size

Treatment

Outcome

F/U

1

50/F

1 y

Elbow

1 cm

Excision

NED

15 mo

2

33/M

N/A

Thenar eminence, forearm (3 lesions)

N/A

None

Spontaneous CR, recurrence 5 y later on hand and foot

5 y

3

66/F

40 y

Hand and forearm

>30 cm

EBT, XRT

CR, recurrence 2 y later, then local control but no CR, died of unrelated causes

11 y

4

49/F

12 y

Foot

>15 cm

XRT

CR, Stage Ia MF 5 y later, treated, now NED

13 y

5

43/F

3 mo

Tongue

0.6 cm

Excision

NED locally, 3 mo later atypical lymphoid infiltrate on back, XRT, now NED

2 y

6

67/F

1 y

Arm

4 cm

XRT

NED

2 y

7

50/M

3 y

Foot (several lesions)

3 cm each

XRT, PUVA, XRT

Two recurrences after two CR, then lost to F/U

8 y

  1. F/U, length of follow-up from diagnosis; F, female; M, male; EBT, electron beam therapy; XRT, local radiation; PUVA, psoralen and UVA; NED, no evidence of disease; N/A, information not available; CR, complete regression.
  2. aDuration of lesion prior to diagnosis.
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