Table 2 Electrophysiological data of dHMN type II patients with the HSP27 mutation. Amplitudes of evoked response are given in parentheses (for motor NCV in mV and for sensory NCV in µV). Normal NCV values: motor median nerve = ≥ 50.5 m/s; ulnar nerve = ≥ 51.1 m/s; peroneal nerve = ≥ 40.5 m/s; tibial nerve = ≥ 41.1 m/s; sensory median nerve = ≥ 39.3 m/s; ulnar nerve = ≥ 37.5 m/s; sural nerve = ≥ 32.1 m/s. Normal amplitude values: motor median nerve = ≥ 6 mV; ulnar nerve = ≥ 8 mV; peroneal nerve = ≥ 1.5 mV; tibial nerve = ≥ 6 mV; sensory median nerve = ≥ 8.8 µV; ulnar nerve = ≥ 7.9 µV; sural nerve = ≥ 6.0 µV. NR, not recordable
From: Distal hereditary motor neuropathy in Korean patients with a small heat shock protein 27 mutation
