VATER association with female hypospadia

Abstract

A six months old female infant was found multiple anomalies and repeatedly admitted to our hospital after birth. Esophageal atresia with distal tracheo-esophageal fistula and duodenal atresia was diagnosed by X-ray and completely surgically repaired. Echocardiography showed truncus arteriosus type Al with persistent ductus arteriosus. The hemodynamic status was temporally stabilized by B-T shunt creation. She had recurrent urinary tract infection. The renal echo showed severe right hydronephrosis and right ureter dilatation at birth which spontaneous regressed after subsequent follow-up. The VCUG showed that the urethral meatos located at anterior vaginal wall. We will present and discuss this rare urogenital condition- female hypospadia with VATER association.