Table 3 Clinical and immunohistochemical characteristics of IgG4+ primary cutaneous marginal zone lymphomas
Case | Site | Gender | Age | IgG4/IgG (%)/ cell count/HPF (mean) | Light chain | Treatment | Relapse | Staging | Borrelia burgdorferi | LDH | Number of lesions at presentation | Clinical presentation of the lesions (nodule vs other) |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
1 | Neck | M | 51 | 99/89 | κ | E | No | NEM | Negative | NA | 1 | Nodule |
2 | Upper extremitiy | M | 70 | 99/218 | λ | E | No | NEM | NA | Elevated | 1 | Nodule |
3 | Lower extremity | M | 32 | 98/124 | κ κ | E, D | Yes | NEM | NA | Normal | 1 | Nodule |
4 | Back | M | 74 | 99/130 | κ | C, PD | Yes | NEM | Positive | Normal | >2 | Nodule |
5 | Back | F | 53 | 95/173 | λ | E | NA | NEM | Negative | Normal | 1 | Nodule |
6 | Back | F | 28 | 83/92 | λ | E, D | yes | NEM | Negative | Normal | 1 | Nodule |
7 | Back | M | 26 | 78/75 | κ | NA | NA | NA | NA | NA | 1 | Nodule |
8 | Shoulder | M | 46 | 96/210 | κ | C, R, PD | NA | NEM | NA | Normal | >2 | Other |
9 | Upper extremitiy | F | 75 | 90/110 | λ | E, R | Yes | NEM | NA | Normal | 1 | Nodule |
10 | Shoulder | M | 69 | 77/124 | λ | E | Yes | NA | NA | NA | NA | Nodule |
11 | Back | F | 58 | 83/110 | κ | R | No | NEM | NA | Normal | 1 | Other |
12 | Shoulder | M | 74 | 76/108 | λ | E | No | NEM | NA | Normal | 1 | Other |
13 | Back | M | 29 | 95/131 | κ | E | Yes | NEM | Negative | Normal | >2 | Nodule |
14 | NA | M | 36 | 84/84 | κ | NA | Yes | NA | NA | NA | 1 | Nodule |
15 | Back | M | 40 | 99/177 | κ | E, R | No | NEM | NA | normal | 1 | Nodule |
16 | Head | F | 55 | 90/100 | κ | NA | Yes | NA | NA | NA | 1 | Nodule |
17 | Upper extremitiy | M | 37 | 96/185 | κ | R | No | NEM | NA | Normal | 1 | Nodule |
18 | Shoulder | M | 80 | 99/111 | κ | NA | NA | NA | NA | NA | 1 | Nodule |
19 | Upper extremitiy | F | 49 | 80/117 | κ | NA | Yes | NA | NA | NA | 1 | Other |
