Fig. 1

Segregation analysis, sanger sequence and MRI manifestation. a MRI image of proband. The arrow indicated the patchy, spot-like, long T1 and T2 signal shadows symmetrically in cerebral peduncles corticospinal tract. The triangle indicated the flakes T2WI in the cerebral bridge. b Segregation analysis of affected individual. Rectangles indicate males, circles female, and solid circle represents affected individual. The proband was pointed out by arrow. c Sanger sequence of the affected family. The arrows indicate mutation sites