Fig. 3: Skeletal muscle mitochondria of Smn1ΔSkm mice show ultrastructural abnormalities.

a Representative electron micrographs of mitochondria from TA muscles of the indicated genotypes. Scale bar: 5 μm. b Representative high magnification of abnormal mitochondria in TA muscle of Smn1ΔSkm mice. Scale bar: 0.5 μm. c Box-dots plots of the number of damaged mitochondria per area of Wt and Smn1ΔSkm TA muscles. The error bars indicate SEM; ***p = 2.8E-12. d Morphometric quantification of the area and perimeter of mitochondria from the different genotypes. >200 mitochondria from Wt and Smn1ΔSkm mice (n = 3) were analyzed. The error bars indicate SEM; ****p ≤ 10E-17.