Fig. 3: Human frataxin interacts with respiratory chain complexes I, II and III in healthy LCLs.

A Representative confocal images of in situ PLA experiments performed as described in the legend of Fig. 1. B Western blotting analysis of co-immunoprecipitation (co-IP) experiments (representative image of one of three independent experiments). Input corresponds to the total cell lysate used for co-IP assay; flow through and final wash represent the fractions eluted from the incubation of cell lysate with the resin and collected after the third wash, respectively. The supernatant containing the IP sample after denaturation of the resin was loaded in the fourth lane. Equal volumes (i.e., 35 μL) of samples were loaded in each lane. Blots were immunodecorated with antibodies against FXN, NDUFS1 (complex I), SDHB (complex II) and UQCRFS1 (complex III).