Table 3 Clinical Outcomes during follow-up according to treatment.

	All	ARB	BB	BB&ARB	celi	celi&ARB	no treatm	p-value
n	126	18	9	73	2	9	15
Arterial events
Patients	26(20.63)	2(11.11)	2(22.22)	15(20.55)	1(50.00)	1(11.11)	5(33.33)
No. events	39	3	3	26	1	1	6	0.5945
Events 5 yrs	1.25(0.78,4.04)	5.60(0.86,10.34)	2.47(0.54,4.40)	1.31(0.67,3.02)	4.87(4.87,4.87)	1.11(1.11,1.11)	1.15(0.77,3.53)	0.9784
Bowel events
Patients	3(2.38)	1(5.56)	0(0.00)	2(2.74)	0(0.00)	0(0.00)	0(0.00)
No. events	3	1	0	2	0	0	0	0.8111
Events 5 years	0.86(0.72,1.86)	2.18(2.18,2.18)	-	0.83(0.68,0.90)	-	-	-	0.2207
Pneumothorax events
Patients	1(0.79)	0(0.00)	1(11.11)	0(0.00)	0(0.00)	0(0.00)	0(0.00)
No. events	1	0	1	0	0	0	0	0.0124
Events 5 years	0.54(0.54,0.54)	-	0.54(0.54,0.54)	-	-	-	-	0.0000
Pulmonary events
Patients	5(3.97)	0(0.00)	2(22.22)	2(2.74)	0(0.00)	1(11.11)	0(0.00)
No. events	5	0	2	2	0	1	0	0.0331
Events 5 years	0.83(0.50,1.66)	-	0.70(0.54,0.86)	0.65(0.47,0.83)	-	2.45(2.45,2.45)	-	0.3012
All events
Patients	31(24.60)	3(16.67)	3(33.33)	17(23.29)	1(50.00)	2(22.22)	5(33.33)
No. events	48	4	6	29	1	2	6	0.7654
Events 5 years	1.61(0.86,3.02)	2.18(0.86,10.34)	1.61(0.86,4.40)	1.31(0.74,2.70)	4.87(4.87,4.87)	1.78(1.11,2.45)	1.15(0.77,3.53)	0.9456
CA score base	0.00(0.00,2.00)	0.00(0.00,1.00)	0.00(0.00,1.00)	0.00(0.00,2.00)	0.00(0.00,0.00)	3.00(0.00,6.50)	0.00(0.00,0.00)
CA score end	0.00(0.00,4.00)	0.00(0.00,1.50)	0.00(0.00,1.50)	0.00(0.00,4.00)	5.00(0.00,10.00)	4.00(0.00,9.00)	0.00(0.00,10.00)
CA score base^a	2(0,5)	2(1,3)	1(0,1)	2(1,7)	0(0,0)	5(5,5)	0(0,8)
CA score end^a	10(4,12)	9(6,11)	2(1,2)	6(3,12)	10(10,10)	10(10,10)	12(10,16)
Death	10(7.94)	1(5.56)	0(0)	4(5.48)	1(50)	0(0)	4(27)
Death (vEDSrelated)	8(6.35)	0(0)	0(0)	3(4.11)	1(50)	0(0)	4(27)

Values are n(%) or median(interquartile range). Fisher exact test for qualitative variables and Kruskal-Wallis test for quantitative variables(celiprolol groups excluded from the test due to low numbers).
^aSample of those with arterial events during follow-up.

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