Table 4 Characteristics and causes of death in the 10 patients who died during follow up.
Time under follow-up on treatment or with no treatment, in months (treatment sequence) | |||||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Sex | Age at death | Proband/ Relative | vEDS variant | Follow up (years) | CA Score (1stseen) | CA Score (endFU) | Cause of death | ARB | BB | BB&ARB | celi | celi&ARB | no treatment |
M | 24 | P | Group I | 1.13 | 10 | 20 | Ruptured renal artery aneurysm | - | - | - | - | - | 13.5 |
M | 29 | R | Group I | 4.34 | 0 | 10 | Ruptured thoracic aorta | - | - | - | - | - | 52.1 |
F | 31 | P | Group I | 4.93 | 0 | 10 | Dissection of thoracic aorta | - | - | - | - | - | 59.1 |
F | 19 | P | Group II | 3.81 | 0 | 12 | Aortic dissection | - | - | - | - | - | 45.8 |
F | 28 | P | Group I | 1.03 | 0 | 10 | Renal infarction, infracolic haematoma | - | - | - | 12.3 | - | |
F | 51 | P | Group I | 2.61 | 10 | 20 | Vessel rupture in abdomen | - | - | 31.3 | - | - | |
M | 19 | R | Group I | 0.27 | 0 | 10 | Aortic dissection | - | - | 3.2 | - | - | |
F | 55 | R | Group I | 2.46 | 1 | 1 | Cancera | - | - | 27.4(2) | - | - | 2.1(1) |
F | 76 | R | Group III | 1.99 | 0 | 0 | Lung cancera | 23.8(2) | - | - | - | - | 0.1(1) |
M | 20 | P | Group I | 5.30 | 7 | 17 | Aortic dissection | - | 31.1(1) | 32.5(2) | - | - | |
