Fig. 1: Pedigree of a North American kindred, initially recruited as two independent families (probands PID V-1, VI-21) showing co-segregation of a novel pathogenic POU4F3 (c.37del) variant and autosomal dominant sensorineural hearing loss.

A Seven-generation pedigree with 38 direct descendants of the pedigree founders with hearing loss are marked with a black symbol. B Electropherogram of the novel POU4F3 c.37del frame-shifting variant (left panel, bottom) compared to reference sequence (left panel, top) and to an unaffected relative (right panel, bottom) compared to reference sequence (right panel, top). PID person ID in the pedigree.