Fig. 2: Sodium dodecyl sulfate polyacrylamide gel electrophoresis (SDS-PAGE) on (pro)collagen extracted from patient skin fibroblasts.

Detection of disulfide-linked α1(I) dimers with SDS-PAGE from extracted (pro)collagen of dermal fibroblasts. In P1 (p.(Arg1014Cys)), an α1(I) dimer, indicated by an arrow, is detected in the intracellular and secreted fraction. In P26 (p.(Arg918Cys)), an α1(I) dimer is detected intracellularly, but not in the medium.