Table 2 Summary of studies on the prevalence of primary Sjögren’s syndrome in the adult population (≥ 18 years old) using the 2002 American-European Consensus Group (AECG) criteria.

Author^Ref	Year	Country	Source of cases	Study design	Population size (N)	pSS cases (N)	Female/male (N)	Prevalence % Prevalence rate (95% CI)/100,000
Maciel et al³	2015	USA (Olmsted County, Minnesota)	Medical record linkage system	Population based	113,306	23	NS	0.02% 22 (1.3–3.1)
Valim et al.⁵	2013	Brazil (Vitoria)	Questionnaire Clinical examination	Cross-sectional population survey	1,205	2	NS	0.06% 60.82 (43.69–77.94)
Anagnostopoulos et al.¹⁰	2010	Greece (Prefecture)	Questionnaire Clinical examination	Cross-sectional population survey	1,705	4	NS	0.23% 234.60 (4.70–464.51)
Birlik et al.¹¹	2009	Turkey (Balcova, Narlidere)	Questionnaire Clinical examination	Population survey	2,887	6	6/0	0.21% 207.83 (41.53–374.12)
Alamanos et al.¹⁴	2006	Greece (north-west Greece)	Personal registry physicians Medical record search	Population based	488,435	422	402/20	0.09% 86.40 (78.16–94.64)
Kabasakal^a et al.¹⁵	2006	Turkey (Bornova)	Questionnaire Clinical examination	Cross-sectional population survey	831	6	NS	0.72% 722.02 (144.29–1,299.75)
Trontzas et al.¹⁶	2005	Greece	Questionnaire Clinical examination	Population survey	8,470	13	NS	0.15% 0.08% ages 44–64 years 0.40% ages > 65 years 148.74 (67.89–229.60)

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