Table 1 Relative amounts of individual mature frataxin proteoforms in mouse tissues (n = 3).
From: Extra-mitochondrial mouse frataxin and its implications for mouse models of Friedreich’s ataxia
Tissue | LGT (N) | N-1 (GTL) | N-2 (TLD) | N-3 (LDN) | N-4 (DNP) | N-5 (NPS) | N-6 (PSS) | |||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
% | SEM | % | SEM | % | SEM | % | SEM | % | SEM | % | SEM | % | SEM | |
Heart | 14.9 | 2.9 | 77.2 | 9.3 | 0.7 | 0.2 | 2.7 | 0.8 | 0.5 | 0.2 | 0.2 | 0.1 | 3.8 | 0.8 |
Brain | 7.3 | 1.7 | 86.9 | 3.4 | 0.3 | 0.2 | 0.1 | 0.1 | 0.7 | 0.3 | 0.1 | 0.1 | 4.6 | 2.6 |
Liver | 11.3 | 2.5 | 47.0 | 8.4 | 2.8 | 1.2 | 36.0 | 4.6 | 1.8 | 0.4 | 0.5 | 0.1 | 0.6 | 0.1 |
