Table 1 Characteristics of ALS patients at the time of collection of baseline data.
Characteristic | Total | Male | Female |
|---|---|---|---|
n (%) | 94 (100) | 64 (68.1) | 30 (31.9) |
Age, year [mean (95% CI)] | 51.82 (49.49–54.15) | 51.72 (48.75–54.69) | 52.03 (48.14–55.92) |
Drinking, n (%) | 24 (25.5) | 21 (32.8) | 3 (10.0) |
Smoking, n (%) | 37 (39.4) | 34 (53.1) | 3 (10.0) |
ALSFRS-R score [median (IQR)] | 39.50 (11.00) | 39.00 (11.00) | 40.00 (10.00) |
ALSFRS-R, Bulbar sub-scores [median (IQR)] | 11.50 (2.00) | 12.00 (2.00) | 10.00 (4.00) |
ALSFRS-R, Resp sub-scores [median (IQR)] | 12.00 (2.00) | 12.00 (2.00) | 11.00 (2.00) |
Weight at screening [mean (95% CI)] | 66.26 (63.97–68.55) | 69.76 (67.10–72.41) | 58.78 (55.65–61.92) |
BMI at screening [mean (95% CI)] | 23.72 (23.03–24.42) | 24.09 (23.23–24.96) | 22.94 (21.79–24.09) |
Duration of disease, months [median (IQR)] | 21.00 (14.75) | 22.00 (13.50) | 20.00 (17.75) |
Diagnostic delay, months [median (IQR)] | 13.83 (13.20) | 12.37 (13.68) | 15.92 (13.73) |
Bulbar onset, n (%) | 15 (16) | 7 (10.9) | 8 (26.7) |