Table 2 Baseline clinical data of 27 untreated patients with IgG4-related disease.

From: Serum IgG4 levels at diagnosis can predict unfavorable outcomes of untreated patients with IgG4-related disease

No

IgG4 (mg/dL)

IgG (mg/dL)

IgE (IU/mL)

Hypocomple-mentemia

Eosinophil count (/µL)

Allergy

Involved organs

Number of involved organs§

IgG4-RD RI

SI

Deterio-ration

1

164

1960

1621

197

+

Sa, La

2

9

2

2150

3310

74

177

+

Sa, La, *K (#M)

3

12

+

+

3

354

1963

764

138

A

1

9

4

196

1487

447

191

+

A, *RF

2

15

+

5

187

1317

134

21

+

Sa, *La

2

9

+

6

73.1

1277

49

180

+

Sa

1

3

7

1230

2655

1668

1014

+

Sa, K, L, S

4

18

8

565

1732

135

113

+

P

1

12

9

2150

3751

4423

149

+

Sa

1

9

10

1520

2938

48

79

#Sa (#La, #K, #A)

1

6

+

11

361

1936

8

+

119

Sa, Ly (#La, #P, #K, #A)

2

9

+

12

1040

2127

227

249

#Sa, A, Ph (#La, #RF)

3

15

+

13

632

1934

328

70

+

La

1

6

14

997

2078.7

1730

150

A, Bi (#P)

2

15

+

15

254

1559.6

745

290

Sa, La, L, Ly

4

15

16

374

1413.9

883

180

+

K

1

6

17

1160

3506

2328

68

+

L (#Sa, #P, #A)

1

18

+

18

1740

4298

324

959

+

Sa (#A, #Pr)

1

15

+

19

292

2141

87

362

P

1

6

20

313

2237

1867

70

*Sa, La, A, Ly, Pec

5

24

+

21

534

1674

86

598

+

Sa, La, *P, *K

4

15

+

22

136

1419

1247

188

+

Sa

1

6

23

133

983

1364

829

+

Sa

1

3

24

185

1924

32,313

2952

+

Sa

1

6

25

297

2213

2042

772

+

Sa, P, K

3

12

26

99.8

1512

NA

121

+

Bi (#*A)

1

6

+

+

27

969

3635

4042

2262

+

K, Bi

2

12

  1. A aortic/arterial lesion, Bi bile duct lesion, IgG serum immunoglobulin G levels, IgG4 serum immunoglobulin G4 levels, IgG4-RD RI immunoglobulin G4-related disease responder index, IgE serum immunoglobulin E levels, K kidney lesion, L lung lesion, La lacrimal grand lesion, Ly lymph node lesion, M mammary lesion, P pancreas lesion, Pec pericarditis, Ph pharyngeal mass, Pr prostate lesion, RF retroperitoneal fibrosis, S skin lesion, Sa salivary gland lesion, SI spontaneous improvement.
  2. *Organ in which spontaneous improvement occur. #Organ in which deterioration occur. ( )De novo organ involvement.
  3. §Number of involved organs at the first diagnosis of IgG4-RD.