Table 2 Anthropometric data, results of spirometry and spiroergometry and Dordel-Koch-Test (DKT) of ARM patients and controls (n = 18 each).

Age

13.6 ± 3.0

13.3 ± 3.1

0.828 $

Gender (male/female)

13/5

13/5

1.000

Anthropometry

Height [m]

1.6 ± 0.1

1.6 ± 0.2

0.419 $

Body weight [kg]

49.7 ± 13.4

47.3 ± 15.8

0.636 $

BMI Z-score

 − 1.6 ± 5.9

 − 0.34 ± 1.1

0.913

Body fat [%]

15.1 ± 8.1

11.1 ± 7.3

0.134 #

Muscle mass [kg/height²]

5.5 ± 1.7^a

6.0 ± 2.1

0.425 $

Spirometry

VC_max [%]

93.9 ± 13.3

102.0 ± 12.5

0.069 $

Tiffeneau Index [%]

86.6 ± 10.2

87.7 ± 5.2

0.695 $

Spiroergometry

Relative performance [%]

110.4 ± 19.2

127.8 ± 16.9

0.007 $

Peak VO₂ [ml/kg/min]

41 ± 8.2

45.6 ± 9.4

0.323 #

O₂/HR [ml]

10.7 ± 3.4

10.8 ± 4.1

0.927 $

EQO₂

20.7 ± 3.1

20.2 ± 2.5

0.557 $

BR

15.0 ± 14.9

19.7 ± 16.0

0.367 $

ΔVO₂/ΔWR

11.4 ± 1.2

11.1 ± 1.3

0.444 $

Dordel–Koch test (DKT)

Lateral jumping

4.1 ± 1.1

2.6 ± 1.1

 < 0.001 #

Sit and reach

3.6 ± 1

3.2 ± 0.9

0.279 #

Sit-ups

3.7 ± 0.9

2.7 ± 0.8

0.008 #

Long stand jump

4.1 ± 1.1

2.8 ± 0.9

0.001 #

One-legged stand

2.2 ± 1.8

1 ± 0

0.091 #

Push-Ups

2.7 ± 1.1

1.9 ± 0.8

0.059 #

DKT

3.4 ± 0.7

2.4 ± 0.5

 < 0.001 #