Table 2 Short-term and long-term audiometric postoperative results following stapes surgery in individuals with osteogenesis imperfecta.

From: Treatments for hearing loss in osteogenesis imperfecta: a systematic review and meta-analysis on their efficacy

Study

Level of evidence

Mean age at primary surgery (range)

Frequency range measured

Short term (≤ 12 months) results

Long term (> 12 months) results

No. of ears

Mean follow up (months)

ABG ≤ 10 dB, no. of ears (%)

10 < ABG < 20 dB, no. of ears (%)

ABG > 20 dB, no. of ears (%)

Mean ABG, dB

Shea and Postma (1982)40

4

–

0.5, 1.0 and 2.0 kHz

51

12

38 (75)

–

–

12

24

84

–

–

–

–

Pedersen (1983)76

4

31

0.5, 1.0, 2.0, and 4.0 kHz

42

3

26 (62)

9 (21)

7 (17)

–

–

–

–

–

–

–

Garretsen and Cremers (1990)43

4

30.6

0.5, 1.0 and 2.0 kHz

52

3

37 (71)

11 (21)

4 (8)

10

37

115

26 (70)

7 (19)

4 (11)

12

Albahnasawy et al. (2001)46

4

36.4 (25–55)

0.5, 1.0, 2.0, and 4.0 kHz

5

6–12

4 (80)

1 (20)

0 (0)

8

–

–

–

–

–

–

Van der Rjit and Cremers (2003)47

4

38

0.5, 1.0 and 2.0 kHz

13

1.5

4 (31)

7 (50)

3 (21)

–

–

–

–

–

–

–

Kuurila et al. (2004)31

4

30.1 (15–53)

0.5, 1.0 and 2.0 kHz

43

6–12

18 (42)

13 (30)

12 (28)

–

–

–

–

–

–

–

Vincent et al. (2005)32

4

37 (18–67)

0.5, 1.0, 2.0, and 4.0 kHz

21

1.5

18 (86)

0 (0)

3 (14)

4

10

24

8 (80)

–

–

5.6

Swinnen et al. (2009)34

4

40 (17–71)

0.5, 1.0, 2.0 and 3.0 kHz

12

1.5

8 (67)

4 (33)

0 (0)

8

8

42

6 (75)

1 (13)

1(13)

9

Swinnen et al. (2012)35

4

32.7 (13–69)

0.5, 1.0, 2.0 and 3.0 kHz

28

2

17 (61)

10 (36)

1 (3)

8.2

18

168

18 (100)

0 (0)

0 (0)

4.8

Vincent et al. (2014)37

4

36 (18–59)

0.5, 1.0, 2.0, and 4.0 kHz

32

4

28 (88)

–

–

4.3

18

26

13 (72)

–

–

4.7

Skarzyński et al. (2019)38

4

32.5 (14–63)

0.5, 1.0, 2.0, and 4.0 kHz

21

–

9 (43)

–

–

12.26

17

–

7 (41)

–

–

11.54

Ma et al. (2020)39

4

28.5 (12–48)

0.5, 1.0, 2.0 and 3.0 kHz

17

–

1 (6)

8 (47)

8 (47)

19

10

36

3 (30)

3 (30)

4 (40)

20

  1. No sufficient data is indicated with a line (-). ABG is Air Bone Gap. Level of evidence 4 refers to well-designed case-series or cohort studies58.
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