Table 6 Short-term (< 12 months) outcomes of cochlear implantations in individuals with osteogenesis imperfecta (OI).
Study | Age at surgery | OI type | Sex | Preoperative speech perception | Postoperative speech perception | Follow-up |
|---|---|---|---|---|---|---|
Szilvássy et al. (1998)67 | 50 | – | F | Wearing a hearing aid closed set speech recognition test revealed invaluably low results | “Significant improvement in hearing” | 7 days |
Huang et al. (1998)77 | 42 | – | F | Wearing a hearing aid: - Word: 12% - Sentence: 24% - Vowel: 60% | - Word: 44% - Sentence: 59% - Vowel: 94% | 3 months |
Migirov et al. (2003)64 | 6 | – | M | Some words identified | OS word identification: - Mono-syllabic words: 25% - Two-syllable words: 40% - Hebrew speech pattern contrast test: 44% | 6 months |
Streubel and Lustig (2005)27 | 35 | Type I | F | - Phoneme score (CNC): 0% - Words score (CNC): 0% - Sentence score (CID): 0% | - Phoneme score (CNC): 75% - Words score (CNC): 54% - Sentence score (CID): 99% | 12 months |
– | Type I | F | - Phoneme score (CNC): 12% - Words score (CNC): 4% - Sentence score (CID): 75% | - Phoneme score (CNC): 83% - Words (CNC): 70% - Sentence score (CID): 100% | 12 months | |
Rotteveel et al. (2008)53 | 45 | Type I | F | – | - Phoneme score: 84% - Word score: 60% NVA-test | 12 months |
51 | Type I | F | – | - Phoneme score: 78% - Word score: 56% NVA-test | 12 months | |
Sainz et al. (2009)65 | – | Type I | – | The electrode guide insertion was arrested and deviated multiple times while attempting the implantation that was averted | – | |
Heo et al. (2009)78 | 39 | – | F | - CS 1-syllable word identification: 0% - OS 1-syllable word identification: 0% - Length of words identification: 8.3% - Word comprehension: 43.55% - Sentence comprehension: 30% | - CS 1-syllable word identification: 100% - OS 1-syllable word identification: 100% - Length of words identification: 100% - Word comprehension: 100% - Sentence comprehension: 100% | 6 months |
Makizumi et al. (2013)66 | 52 | – | F | Wearing a hearing aid: Phonemes 10% | - Monosyllables: 62% - Words 79% - Sentences: 91% | 6 months |
Marfatia et al. (2020)54 | 14 | – | F | – | Word recognition score 45% at 60 dB | 12 months |
