Table 1 Baseline characteristics of FD patients.

From: Increased cardiac involvement in Fabry disease using blood-corrected native T1 mapping

Characteristic

Total (n = 218)

Females (n = 118)

Males (n = 100)

Female sex, n (%)

118 (54)

  

Age, years

46 ± 15

45 ± 14

46 ± 16

Height, cm

169 ± 9

166 ± 8

173 ± 10

Weight, kg

71 ± 14

70 ± 14

72 ± 14

BSA, m2

1.8 ± 0.2

1.8 ± 0.2

1.9 ± 0.2

LVEDV, ml

129 ± 34

121 ± 23

138 ± 41

LVEDVI, ml/m2

71 ± 15

68 ± 11

74 ± 19

LVESV, ml

36 ± 18

32 ± 13

41 ± 21

LVESVI, ml/m2

20 ± 9

18 ± 7

22 ± 10

LVSV, ml

93 ± 23

89 ± 16

97 ± 29

LVSVI, ml/m2

51 ± 11

50 ± 8

52 ± 14

LVEF, %

73 ± 9

74 ± 8

71 ± 19

LVM, g

162 ± 78

135 ± 59*

193 ± 86

LVMI, g/m2

88 ± 39

75 ± 30

104 ± 42

Hematocrit

40 ± 4

39 ± 3†

42 ± 4‡

On ERT, %

47%*

42%

59%*

  1. Data presented as mean ± SD.
  2. BSA body surface area, ERT enzyme replacement therapy, LVEDV left ventricular end diastolic volume, LVESV left ventricular end systolic volume, LVSV left ventricular stroke volume, LVEF ejection fraction, LVM left ventricular mass, I signifies indexed to BSA.
  3. *Data missing for n = 3, †n = 30 and, ‡n = 39 patients.
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