Fig. 1

Best-corrected binocular visual acuity (BCVA) of 20 patients per age at last follow-up.Mean BCVA was 0.42 LogMAR (20/52 Snellen), median 0.34 LogMAR (20/43 Snellen) and range 0-2. Seventy five percent of the patients had a BCVA lower than 0.58 LogMAR (20/76 Snellen). *Patient 9 had, in addition to optic atrophy, corneal band keratopathy in the left eye and vitreomacular traction in both eyes but was not treated operatively because potential visual gain was expected to be insignificant.