Table 1 Characteristics of study participants by cardiomyopathy severity.
| Â | Total | Severe Cardiomyopathy | Less Severe Cardiomyopathy |
|---|---|---|---|
Participants | 54 | 18 (33%) | 36 (67%) |
Sibling Participants | 31 | 10 (32%) | 21 (68%) |
Siblings with Concordant Cardiomyopathy Severity | 18 | 4 (22%) | 14 (78%) |
Siblings with Discordant Cardiomyopathy Severity | 13 | 6 (46%) | 7 (54%) |
Individuals with no Relatives in the Study | 23 | 8 (35%) | 15 (65%) |
Number with Full cMRI Data Available | 48 | 15 | 33 |
Average Age at Most Recent cMRI in Years | 14.5 | 15.7 | 13.9 |
Average LVEF by Most Recent cMRI | 52.4% | 39.3% | 58.4% |
Number with LGE Observed (%) | 40 (74.1%) | 16 (88.9%) | 24 (66.7%) |
Average Age of LGE on cMRI in Years | 14.4 | 14.8 | 14.2 |
Documented Deaths (%) | 13 (24.1%) | 12 (66.7%) | 1 (2.8%) |
Average Age at Death in Years (Range) | 19.9 (14.7-26.1) | 19.6 (14.7-26.1) | 23.0 |
