Table 2 Cardiac characteristics of study participant subgroups by cardiomyopathy severity.
| Â | Concordant Sibling Cohort | Discordant Sibling Cohort | Unrelated Participants Cohort | |||
|---|---|---|---|---|---|---|
| Â | Severe | Less Severe | Severe | Less Severe | Severe | Less Severe |
n | 4 | 14 | 6 | 7 | 8 | 15 |
Number with Full cMRI Data Available | 4 (100%) | 12 (85.7%) | 5 (83.3%) | 6 (85.7%) | 6 (75%) | 15 (100%) |
Average Age at Most Recent cMRI in Years | 18.0 | 12.6 | 15.5 | 12.6 | 11.1 | 18.8 |
Average LVEF by Most Recent cMRI | 36% | 61.4% | 45% | 55.5% | 36.8% | 57.1% |
Number with LGE Observed (%) | 4 (100%) | 7 (50%) | 6 (100%) | 5 (71.4%) | 6 (75%) | 12 (80%) |
Average Age of LGE on cMRI in Years | 15.0 | 10.7 | 14.2 | 17.2 | 15.1 | 15.5 |
Documented Deaths (%) | 2 (50%) | 0 | 3 (50%) | 0 | 7 (87.5%) | 1 (6.7%) |
Average Age at Death in Years | 25.6 | NA | 18.3 | NA | 18.5 | 23.1 |
